Disturbance of cultured rat neuronal network activity depends on concentration and ratio of leucine and α-ketoisocaproate: Implication for acute encephalopathy of maple syrup urine disease

Pediatric Research

Volumn 53, Issue 2, 2003, Pages 320-324

  Görtz, Philipp ^a   Köller, Hubertus ^a   Schwahn, Bernd ^a   Wendel, Udo ^a   Siebler, Mario ^a  

^a HEINRICH HEINE UNIVERSITY   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

2 OXOISOCAPROIC ACID; 4 AMINOBUTYRIC ACID; GLUTAMIC ACID; GLYCINE; LEUCINE; NEUROTRANSMITTER;

4 AMINOBUTYRIC ACID RELEASE; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BLOOD LEVEL; CALCIUM CELL LEVEL; CEREBROSPINAL FLUID; CONCENTRATION RESPONSE; CONTROLLED STUDY; ELECTROPHYSIOLOGY; EMBRYO; GABAERGIC SYSTEM; MAPLE SYRUP URINE DISEASE; MEMBRANE CURRENT; MEMBRANE STEADY POTENTIAL; NERVE CELL NETWORK; NEUROTRANSMITTER RELEASE; NONHUMAN; POTASSIUM CURRENT; PRESYNAPTIC NERVE; PRIORITY JOURNAL; RAT; SODIUM CURRENT;

ANIMALS; CELLS, CULTURED; CULTURE MEDIA; DOSE-RESPONSE RELATIONSHIP, DRUG; ELECTROPHYSIOLOGY; KETO ACIDS; LEUCINE; MAPLE SYRUP URINE DISEASE; MEMBRANE POTENTIALS; NEOCORTEX; NERVE NET; NEURONS; PATCH-CLAMP TECHNIQUES; POTASSIUM CHANNELS, VOLTAGE-GATED; RATS;

EID: 0037313335     PISSN: 00313998     EISSN: None     Source Type: Journal    
DOI: 10.1203/01.PDR.0000047521.50656.16     Document Type: Article

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