Acute inflammatory demyelinating polyradiculoneuropathy associated with perforin-deficient familial haemophagocytic lymphohistiocytosis

Acta Paediatrica, International Journal of Paediatrics

Volumn 92, Issue 3, 2003, Pages 398-401

  Del Giudice, E ^a   Savoldi, G ^b   Notarangelo, L D ^b   Di Benedetto, L ^a   Manganelli, F ^a   Bruzzese, E ^a   Romano, A ^a   Santoro, L ^a  

^a UNIVERSITY OF NAPLES FEDERICO II   (Italy)

^b UNIVERSITY OF BRESCIA   (Italy)

Author keywords

Acute inflammatory demyelinating polyneuropathy; Epstein Barr virus; Familial haemophagocytic lymphohistiocytosis; Guillain Barr ; Perforin gene defects; Syndrome

Indexed keywords

PERFORIN; VIRUS DNA;

ACUTE INFLAMMATORY DEMYELINATING POLYRADICULONEUROPATHY; ARTICLE; CASE REPORT; CHILD; DEMYELINATING DISEASE; DISEASE ASSOCIATION; EPSTEIN BARR VIRUS; ERYTHROPHAGOCYTOSIS; FAMILIAL DISEASE; GENE MUTATION; GUILLAIN BARRE SYNDROME; HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; HISTIOCYTOSIS; HUMAN; MALE; NEUROLOGIC DISEASE; PRIORITY JOURNAL;

CHILD; FATAL OUTCOME; GUILLAIN-BARRE SYNDROME; HISTIOCYTOSIS, NON-LANGERHANS-CELL; HUMANS; MALE; MEMBRANE GLYCOPROTEINS; PORE FORMING CYTOTOXIC PROTEINS;

EID: 0037251820     PISSN: 08035253     EISSN: None     Source Type: Journal    
DOI: 10.1080/08035250310009374     Document Type: Article

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