Congenital erythropoietic porphyria associated with myelodysplasia presenting in a 72-year-old man: Report of a case and review of the literature

British Journal of Dermatology

Volumn 148, Issue 1, 2003, Pages 160-164

  Kontos, A P ^a   Ozog, D ^a   Bichakjian, C ^b   Lim, H W ^a,c  

^a HENRY FORD HEALTH SYSTEM   (United States)

^b UNIVERSITY OF MICHIGAN HEALTH SYSTEM   (United States)

^c HENRY FORD HOSPITAL   (United States)

Author keywords

Congenital erythropoietic porphyria; G nther's disease; Myelodysplasia; Photosensitivity; Uroporphyrinogen III synthase

Indexed keywords

ANTIPRURITIC AGENT; BETA CAROTENE; CINNAMIC ACID; LUMITENE; SUNSCREEN; UROPORPHYRINOGEN III SYNTHASE; ZINC OXIDE;

AGED; ANAMNESIS; ARTICLE; BONE MARROW; CASE REPORT; CLINICAL FEATURE; CONGENITAL ERYTHROPOIETIC PORPHYRIA; CYTOGENETICS; DISEASE ASSOCIATION; HUMAN; LABORATORY TEST; MALE; MYELODYSPLASIA; ONSET AGE; PHOTOSENSITIVITY; PHYSICAL EXAMINATION; PRIORITY JOURNAL; PROTECTIVE CLOTHING; SIDEROBLASTIC ANEMIA; SKIN DISEASE; THROMBOCYTOPENIA;

AGED; HUMANS; MALE; MYELODYSPLASTIC SYNDROMES; PORPHYRIA, ERYTHROPOIETIC; PORPHYRINS;

EID: 0037244080     PISSN: 00070963     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1365-2133.2003.05040.x     Document Type: Article

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