Porphyrins in urine, plasma, erythrocytes, bile and faeces in a case of congenital erythropoietic porphyria (Gunther's disease) treated with blood transfusion and iron chelation: Lack of benefit from oral charcoal

Biomedical Chromatography

Volumn 12, Issue 6, 1998, Pages 350-356

  Gorchein, Abel ^a   Guo, Rong ^b   Lim, Chang Kee ^b   Raimundo, Ana ^c   Pullon, Humphrey W H ^d   Bellingham, Alastair J ^e  

^a IMPERIAL COLLEGE SCHOOL OF MEDICINE   (United Kingdom)

^b UNIVERSITY OF LEICESTER   (United Kingdom)

^c CENTRAL MIDDLESEX HOSPITAL   (United Kingdom)

^d PALMERSTON NORTH HOSPITAL   (New Zealand)

^e KING'S COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

BLOOD; CHARCOAL; IRON;

BLOOD TRANSFUSION; CLINICAL FEATURES; CLINICAL SYNDROMES; DECARBOXYLASES; GENETIC DISORDERS; IRON CHELATION; SYNTHASES; TRACE AMOUNTS; UROPORPHYRINOGEN III;

PORPHYRINS;

CHARCOAL; COPROPORPHYRIN; PORPHYRIN; UROPORPHYRIN; UROPORPHYRINOGEN III SYNTHASE;

ADULT; ARTICLE; BILE; BLOOD TRANSFUSION; CASE REPORT; CHELATION; CONGENITAL ERYTHROPOIETIC PORPHYRIA; ERYTHROCYTE; FECES; FECES ANALYSIS; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; HUMAN; MALE; URINE LEVEL;

EID: 0031742784     PISSN: 02693879     EISSN: None     Source Type: Journal    
DOI: 10.1002/(SICI)1099-0801(199811/12)12:6<350::AID-BMC761>3.0.CO;2-B     Document Type: Article

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