Correction of the copper transport defect of Menkes patient fibroblasts by expression of two forms of the sheep Wilson ATPase

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1588, Issue 2, 2002, Pages 189-194

  Lockhart, Paul J ^a   La Fontaine, Sharon ^a   Firth, Stephen D ^a   Greenough, Mark ^b   Camakaris, James ^b   Mercer, Julian F B ^a  

^a DEAKIN UNIVERSITY   (Australia)

^b UNIVERSITY OF MELBOURNE   (Australia)

Author keywords

ATP7B; Copper metabolism; P type ATPase

Indexed keywords

ADENOSINE TRIPHOSPHATASE 7B; COMPLEMENTARY DNA; COPPER; ISOENZYME; UNCLASSIFIED DRUG;

ARTICLE; CASE REPORT; CELL IMMORTALIZATION; FIBROBLAST CULTURE; GENETIC CODE; GENETIC TRANSFECTION; HUMAN; HUMAN CELL; MENKES SYNDROME; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; SHEEP; WILSON DISEASE;

ADENOSINE TRIPHOSPHATASES; ANIMALS; BLOTTING, WESTERN; CATION TRANSPORT PROTEINS; CELLS, CULTURED; COPPER; COPPER RADIOISOTOPES; FIBROBLASTS; HUMANS; MEMBRANE PROTEINS; MENKES KINKY HAIR SYNDROME; MICROSCOPY, FLUORESCENCE; SHEEP; TRANSFECTION;

MAMMALIA; OVIS; OVIS ARIES;

EID: 0037145714     PISSN: 09254439     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0925-4439(02)00164-3     Document Type: Article

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