A conditional mutation affecting localization of the Menkes disease copper ATPase: Suppression by copper supplementation

Journal of Biological Chemistry

Volumn 277, Issue 46, 2002, Pages 44079-44084

  Kim, Byung Eun ^a   Smith, Kathryn ^a   Meagher, Carisa K ^a   Petris, Michael J ^a  

^a University of Missouri   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CELL MEMBRANES; CELLS; COPPER; ENZYMES; METABOLISM;

MUTATIONS;

BIOCHEMISTRY;

ADENOSINE TRIPHOSPHATASE; COPPER; COPPER ADENOSINE TRIPHOSPHATASE; GLYCEROL; PROTEIN MNK; UNCLASSIFIED DRUG;

AMINO TERMINAL SEQUENCE; ARTICLE; BINDING SITE; CELL GROWTH; COPPER METABOLISM; DIET SUPPLEMENTATION; ENDOPLASMIC RETICULUM; ENZYME LOCALIZATION; GENETIC TRANSFECTION; HUMAN; HUMAN CELL; MENKES SYNDROME; MUTATION; PRIORITY JOURNAL; PROTEIN FOLDING; PROTEIN LOCALIZATION; PROTEIN SECRETION; TEMPERATURE; TRANS GOLGI NETWORK; X CHROMOSOME LINKED DISORDER;

ADENOSINE TRIPHOSPHATASES; BINDING SITES; CATION TRANSPORT PROTEINS; CELL LINE; CELL MEMBRANE; COPPER; ENDOPLASMIC RETICULUM; FIBROBLASTS; GLYCOSYLATION; HUMANS; IMMUNOBLOTTING; MENKES KINKY HAIR SYNDROME; MICROSCOPY, FLUORESCENCE; MUTATION; PROTEIN BINDING; PROTEIN FOLDING; RECOMBINANT FUSION PROTEINS; TEMPERATURE; TRANSFECTION;

EID: 0037113890     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M208737200     Document Type: Article

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