A Molecular Link between the Common Phenotypes of Type 1 Glycogen Storage Disease and HNF1α-null Mice

Journal of Biological Chemistry

Volumn 276, Issue 11, 2001, Pages 7963-7967

  Hiraiwa, Hisayuki ^a   Pan, Chi Jiunn ^a   Lin, Baochuan ^a   Akiyama, Taro E ^b   Gonzalez, Frank J ^b   Chou, Janice Yang ^a,c  

^a EUNICE KENNEDY SHRIVER NATIONAL INSTITUTE OF CHILD HEALTH AND HUMAN DEVELOPMENT   (United States)

^b NATIONAL CANCER INSTITUTE   (United States)

^c NATIONAL INSTITUTES OF HEALTH   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

DISEASES; GLUCOSE; GROWTH KINETICS; INSULIN; METABOLISM; PATIENT MONITORING; PHOSPHATES; RNA;

ENDOPLASMIC RETICULUM; TRANSACTIVATION;

BIOCHEMISTRY;

CARRIER PROTEIN; GLUCOSE 6 PHOSPHATASE; GLUCOSE 6 PHOSPHATE; GLYCOGEN; INSULIN; MESSENGER RNA; ANTIPORTER; DNA BINDING PROTEIN; GLUCOSE 6 PHOSPHATE(TRANSPORTER); GLUCOSE 6-PHOSPHATE(TRANSPORTER); GLUCOSE TRANSPORTER; HEPATOCYTE NUCLEAR FACTOR 1; HEPATOCYTE NUCLEAR FACTOR 1ALPHA; HEPATOCYTE NUCLEAR FACTOR 1BETA; NUCLEAR PROTEIN; PHOSPHOTRANSFERASE; SLC37A4 PROTEIN, HUMAN; SLC37A4 PROTEIN, MOUSE; TCF1 PROTEIN, HUMAN; TCF1 PROTEIN, MOUSE; TCF2 PROTEIN, HUMAN; TCF2 PROTEIN, MOUSE; TRANSCRIPTION FACTOR;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; GLUCOSE HOMEOSTASIS; GLYCOGEN METABOLISM; GLYCOGEN STORAGE DISEASE TYPE 1; HUMAN; HUMAN CELL; INSULIN RELEASE; MOUSE; NONHUMAN; PATHOPHYSIOLOGY; PHENOTYPE; PRIORITY JOURNAL; SIGNAL TRANSDUCTION; TRANSCRIPTION REGULATION; ANIMAL; GENETICS; METABOLISM; MOUSE MUTANT; PHYSIOLOGY; PROMOTER REGION; TRANSACTIVATION;

ANIMALIA;

ANIMALS; ANTIPORTERS; DNA-BINDING PROTEINS; GLUCOSE-6-PHOSPHATASE; GLYCOGEN STORAGE DISEASE TYPE I; HEPATOCYTE NUCLEAR FACTOR 1; HEPATOCYTE NUCLEAR FACTOR 1-ALPHA; HEPATOCYTE NUCLEAR FACTOR 1-BETA; HUMANS; MICE; MICE, KNOCKOUT; MONOSACCHARIDE TRANSPORT PROTEINS; NUCLEAR PROTEINS; PHENOTYPE; PHOSPHOTRANSFERASES; PROMOTER REGIONS (GENETICS); RNA, MESSENGER; TRANS-ACTIVATION (GENETICS); TRANSCRIPTION FACTORS;

EID: 0035896576     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M010523200     Document Type: Article

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