Hepatocyte nuclear factor 1 inactivation results in hepatic dysfunction, phenylketonuria, and renal Fanconi syndrome

Cell

Volumn 84, Issue 4, 1996, Pages 575-585

  Pontoglio, Marco ^a   Barra, Jacqueline ^a   Hadchouel, Michelle ^b   Doyen, Antonia ^a   Kress, Chantal ^a   Bach, Joséphine Poggi ^c   Babinet, Charles ^a   Yaniv, Moshe ^a  

^a CNRS   (France)

^b INSERM   (France)

^c BICÊTRE HOSPITAL   (France)

Author keywords

[No Author keywords available]

Indexed keywords

ALBUMIN; ALPHA 1 ANTITRYPSIN; FIBRINOGEN; GLUCOSE; NUCLEAR FACTOR I; PHENYLALANINE 4 MONOOXYGENASE;

ALLELE; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; ENZYME DEFICIENCY; FAILURE TO THRIVE; FANCONI RENOTUBULAR SYNDROME; GENE EXPRESSION; HEPATOMEGALY; HOMEOBOX; KIDNEY PROXIMAL TUBULE; LIVER DYSFUNCTION; MOUSE; NONHUMAN; PHENYLKETONURIA; PRIORITY JOURNAL; TRANSCRIPTION INITIATION;

EID: 0030031453     PISSN: 00928674     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0092-8674(00)81033-8     Document Type: Article

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