Treatment of acute porphyria

Hospital Medicine

Volumn 62, Issue 7, 2001, Pages 422-425

  Elder, George H ^a,b   Hift, Richard J ^a  

^a CARDIFF UNIVERSITY   (United Kingdom)

^b UNIVERSITY OF CAPE TOWN   (South Africa)

Author keywords

[No Author keywords available]

Indexed keywords

ARGININE; HEME; HEME ARGINATE; NARCOTIC ANALGESIC AGENT; PORPHOBILINOGEN;

ACUTE INTERMITTENT PORPHYRIA; ADOLESCENT; ADULT; CARBOHYDRATE DIET; CLINICAL TRIAL; FEMALE; HUMAN; MALE; PREGNANCY; PREGNANCY COMPLICATION; REVIEW; TREATMENT OUTCOME; URINE;

ADOLESCENT; ADULT; ANALGESICS, OPIOID; ARGININE; CLINICAL TRIALS; DIETARY CARBOHYDRATES; FEMALE; HEME; HUMANS; MALE; PORPHOBILINOGEN; PORPHYRIA, ACUTE INTERMITTENT; PREGNANCY; PREGNANCY COMPLICATIONS; TREATMENT OUTCOME;

EID: 0035406880     PISSN: 14623935     EISSN: None     Source Type: Journal    
DOI: 10.12968/hosp.2001.62.7.1613     Document Type: Article

References (18)

1. Adrogue HJ, Madias NE (2000) Hyponatraemia. N Engl J Med 342: 1581-9
2. Anderson KE, Spitz IM, Bardin CW, Kappas A (1990) A gonadotropin releasing hormone analogue prevents cyclical attacks of porphyria. Arch Intern Med 150: 1469-74
3. Bonkovsky HL (1993) Advances in understanding and treating 'The little imitator', acute porphyria. Gastroenterology 105: 590-4
4. Bonkovsky HL, Barnard GF (1998) Diagnosis of porphyric syndromes: a practical approach in the era of molecular biology. Semin Liver Dis 18: 57-66
5. Bonkovsky HL, Tschudy DP, Collins A et al (1971) Repression of the overproduction of porphyrin precursors in acute intermittent porphyria by intravenous infusions of hematin. Proc Natl Acad Sci 68: 2725-9
6. Brodie MJ, Moore MR, Thompson GG, Goldberg A (1977) The treatment of acute intermittent porphyria with laevulose. Clin Sci Mol Med 53: 365-71
7. Dover SB, Moore MR, Fitzsimmons EJ. Graham A, McColl KEL (1993) Tin protoporphyrin prolongs the biochemical remission produced by heme arginate in acute hepatic porphyria. Gastroenterology 105: 500-6
8. Elder GH, Smith SG, Smyth SJ (1990) Laboratory investigation of the porphyrias. Ann Clin Biochem 27: 395-42
9. Elder GH, Hift RJ, Meissner PN (1997) The acute porphyrias. Lancet 349: 1613-7
10. Gorchein A (1997) Drug treatment in acute porphyria. Br J Clin Pharmacol 44: 427-34
11. Herrick AL, McColl KEL, Moore MR, Cook A, Goldberg A (1989) Controlled trial of haem arginate in acute hepatic porphyria. Lancet i: 1295-7
12. Kaiman DR, Bonkovsky HL (1998) Management of acute attacks in the porphyrias. Clin Dermatol 16: 299-306
13. Kappas A, Sassa S, Galbraith RA, Nordmann Y (1995) The porphyrias. In: Scriver CR, Beaudet AL, Sly WS, Valle D, eds. The Metabolic and Molecular Bases of Inherited Disease. 7th edn. McGraw-Hill, New York: 2103-59
14. Lindberg RLP, Martini R, Baumgartner M et al (1999) Motor neuropathy in porphobilinogen deaminase-deficient mice imitates the peripheral neuropathy of human acute porphyria. J Clin Invest 103: 1127-34
15. Mustajoki P, Nordmann Y (1993) Early administration of heme arginate for acute porphyric attacks. Arch Intern Med 153: 2004-8
16. Robert TL. Varella L, Meguid MM (1994) Nutrition management of acute intermittent porphyria. Nutrition 10: 551-5
17. Tenhunen R, Mustajoki P (1998) Acute porphyria: treatment with heme. Semin Liver Dis 18: 53-6
18. Thadani H, Deacon A, Peters T (2000) Diagnosis and management of porphyria. Br Med J 320: 1647-51