Motor neuropathy in porphobilinogen deaminase-deficient mice imitates the peripheral neuropathy of human acute porphyria

Journal of Clinical Investigation

Volumn 103, Issue 8, 1999, Pages 1127-1134

  Lindberg, Raija L P ^a   Martini, Rudolf ^b   Baumgartner, Matthias ^a   Erne, Beat ^c   Borg, Jacques ^d   Zielasek, Jürgen ^b   Ricker, Kenneth ^b   Steck, Andreas ^c   Toyka, Klaus V ^b   Meyer, Urs A ^a  

^a UNIVERSITY OF BASEL   (Switzerland)

^b UNIVERSITY OF WÜRZBURG   (Germany)

^c UNIVERSITY HOSPITAL BASEL   (Switzerland)

^d Neurofit SA   (France)

Author keywords

[No Author keywords available]

Indexed keywords

PORPHOBILINOGEN DEAMINASE;

ACUTE INTERMITTENT PORPHYRIA; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; DEMYELINATION; ENZYME DEFICIENCY; ENZYME INDUCTION; ENZYME SPECIFICITY; FEMORAL NERVE; HEME SYNTHESIS; MENSTRUAL CYCLE; MOTOR COORDINATION; MOTOR NEUROPATHY; MOUSE; MUSCLE WEAKNESS; NERVE DEGENERATION; NONHUMAN; PERIPHERAL NEUROPATHY; PRIORITY JOURNAL; SCHWANN CELL;

EID: 0033560646     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI5986     Document Type: Article

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