Lysosomal acid lipase-deficient mice: Depletion of white and brown fat, severe hepatosplenomegaly, and shortened life span

Journal of Lipid Research

Volumn 42, Issue 4, 2001, Pages 489-500

  Du, H ^a   Heur, M ^a   Duanmu, M ^a   Grabowski, G A ^a   Hui, D Y ^a   Witte, D P ^a   Mishra, J ^a  

^a CINCINNATI CHILDREN S HOSPITAL RESEARCH FOUNDATION   (United States)

Author keywords

Cholesteryl ester storage disease; Fatty liver; Wolman disease

Indexed keywords

ACID LIPASE; CHOLESTEROL; CHOLESTEROL ESTER; FATTY ACID; INSULIN;

ADIPOCYTE; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BODY WEIGHT; BROWN ADIPOSE TISSUE; CALORIC INTAKE; CELL DIFFERENTIATION; CHOLESTEROL ESTER STORAGE DISEASE; CHOLESTEROL METABOLISM; CONTROLLED STUDY; ENZYME DEFICIENCY; FATTY ACID BLOOD LEVEL; FATTY ACID METABOLISM; FATTY LIVER; HEPATOSPLENOMEGALY; INSULIN BLOOD LEVEL; KUPFFER CELL; LIPID METABOLISM; LIPID STORAGE; LIVER CELL; LIVER LYSOSOME; MOUSE; NONHUMAN; PRIORITY JOURNAL; WHITE ADIPOSE TISSUE; WOLMAN DISEASE;

ADIPOCYTES; ADIPOSE TISSUE; ADIPOSE TISSUE, BROWN; AGING; ANIMALS; BLOOD GLUCOSE; CELL DIFFERENTIATION; CHOLESTEROL ESTER STORAGE DISEASE; CHOLESTEROL ESTERS; HEPATOMEGALY; HUMANS; INSULIN RESISTANCE; INTESTINES; LIPASE; LIPOPROTEINS; LIVER; LYMPH NODES; LYSOSOMES; MALE; MICE; MICE, KNOCKOUT; SPLEEN; SPLENOMEGALY; TRIGLYCERIDES; WOLMAN DISEASE;

EID: 0035064152     PISSN: 00222275     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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