Difference in substrate specificity between human and mouse lysosomal acid lipase: Low affinity for cholesteryl ester in mouse lysosomal acid lipase

Biochimica et Biophysica Acta - Molecular and Cell Biology of Lipids

Volumn 1487, Issue 2-3, 2000, Pages 155-162

  Groener, Johanna E M ^a   Bax, Wim ^a   Stuani, Cristiana ^b   Pagani, Franco ^b  

^a LEIDEN UNIVERSITY MEDICAL CENTER   (Netherlands)

^b INTERNATIONAL CENTRE FOR GENETIC ENGINEERING AND BIOTECHNOLOGY   (Italy)

Author keywords

Acid lipase; Cholesteryl ester; Cholesteryl ester storage disease; Lysosome; Triacylglycerol; Wolman's disease

Indexed keywords

ACID LIPASE; CHOLESTEROL ESTER; LYSOSOME ENZYME; TRIACYLGLYCEROL;

ANIMAL CELL; ARTICLE; BINDING AFFINITY; CATALYSIS; CHOLESTEROL ESTER STORAGE DISEASE; CONTROLLED STUDY; ENDOCYTOSIS; ENZYME ACTIVITY; ENZYME SPECIFICITY; FIBROBLAST; HELA CELL; HUMAN; HUMAN CELL; LIPID METABOLISM; LIPOLYSIS; NONHUMAN; PRIORITY JOURNAL;

ANIMAL; CELLS, CULTURED; CHOLESTEROL ESTERASE; CHOLESTEROL ESTERS; COMPARATIVE STUDY; FIBROBLASTS; HELA CELLS; HUMAN; LIPASE; LIPOPROTEINS, LDL CHOLESTEROL; LYSOSOMES; MICE; PLASMIDS; SUBSTRATE SPECIFICITY;

EID: 0034721518     PISSN: 13881981     EISSN: None     Source Type: Journal    
DOI: 10.1016/S1388-1981(00)00091-3     Document Type: Article

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