The dystrophin complex forms a mechanically strong link between the sarcolemma and costameric actin

Journal of Cell Biology

Volumn 150, Issue 5, 2000, Pages 1209-1214

  Rybakova, Inna N ^a   Patel, Jitandrakumar R ^a   Ervasti, James M ^a,b  

^a UNIVERSITY OF WISCONSIN SCHOOL OF MEDICINE AND PUBLIC HEALTH   (United States)

^b Dept of Physiology   (United States)

Author keywords

Actin; Costameres; Dystrophin; Membrane skeleton; Muscular dystrophy

Indexed keywords

ALPHA ACTININ; DYSTROGLYCAN; DYSTROPHIN; UTROPHIN; VINCULIN;

ACTIN FILAMENT; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; CYTOSKELETON; HUMAN; HUMAN CELL; MEMBRANE DAMAGE; MEMBRANE STABILIZATION; MOUSE; MUSCULAR DYSTROPHY; NONHUMAN; PRIORITY JOURNAL; SARCOLEMMA; SKELETAL MUSCLE;

ACTINS; ANIMALS; DYSTROPHIN; MICE; MICE, INBRED C57BL; MICE, INBRED MDX; MODELS, BIOLOGICAL; MUSCLE FIBERS; MUSCLE, SKELETAL; SARCOLEMMA;

ANIMALIA;

EID: 0034605070     PISSN: 00219525     EISSN: None     Source Type: Journal    
DOI: 10.1083/jcb.150.5.1209     Document Type: Article

References (35)

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5. Interactions between dystrophin and the sarcolemma membrane
6. Chimaeric mice deficient in dystroglycans develop muscular dystrophy and have disrupted myoneural synapses
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28. Dystrophin colocalizes with β-spectrin in distinct subsarcolemmal domains in mammalian skeletal muscle
29. Dystrophin-glycoprotein complex is monomeric and stabilizes actin filaments in vitro through a lateral association
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