Dystonin-deficient mice exhibit an intrinsic muscle weakness and an instability of skeletal muscle cytoarchitecture

Developmental Biology

Volumn 210, Issue 2, 1999, Pages 367-380

  Dalpé, Gratien ^b   Mathieu, Martine ^a   Comtois, Alain ^b   Zhu, Ercheng ^b   Wasiak, Sylwia ^b   De Repentigny, Yves ^a   Leclerc, Nicole ^c   Kothary, Rashmi ^a  

^a OTTAWA HOSPITAL RESEARCH INSTITUTE   (Canada)

^b Institut du Cancer de Montreal   (Canada)

^c UNIVERSITÉ DE MONTRÉAL   (Canada)

Author keywords

Actin binding.; Cytoskeleton; Desmin; Dystonia musculorum; Dystonin Bpag1; Intermediate filament; Linker protein; Mouse; Muscle

Indexed keywords

ACTIN; COMPLEMENTARY DNA; DESMIN;

ANIMAL CELL; ANIMAL TISSUE; ARTICLE; CELL CULTURE; CELL DIFFERENTIATION; CELLULAR DISTRIBUTION; CROSS LINKING; CYTOARCHITECTURE; MITOCHONDRION; MOUSE; MUSCLE DEVELOPMENT; MUSCLE FIBRIL; MUSCLE ISOMETRIC CONTRACTION; MUSCLE WEAKNESS; MYOBLAST; MYOTUBE; NERVE DEGENERATION; NONHUMAN; PRIORITY JOURNAL; SARCOLEMMA; SKELETAL MUSCLE; ULTRASTRUCTURE;

EID: 0033564136     PISSN: 00121606     EISSN: None     Source Type: Journal    
DOI: 10.1006/dbio.1999.9263     Document Type: Article

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