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Volumn 23, Issue 4, 2000, Pages 697-701

Clinical and biochemical findings in 7 patients with X-linked adrenoleukodystrophy treated with Lorenzo's Oil

Author keywords

[No Author keywords available]

Indexed keywords

ACETIC ACID DERIVATIVE; FISH OIL; HEXACOSANOIC ACID; LIGNOCERIC ACID; LINOLEIC ACID; LINOLENIC ACID; LORENZO OIL; MEVINOLIN; MINERAL; MULTIVITAMIN; PHENYLACETATE SODIUM; UNCLASSIFIED DRUG; VERY LONG CHAIN FATTY ACID;

EID: 0034431520     PISSN: 14154757     EISSN: None     Source Type: Journal    
DOI: 10.1590/S1415-47572000000400001     Document Type: Article
Times cited : (2)

References (17)
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  • 3
    • 0029082884 scopus 로고
    • Adrenoleukodystrophy: Natural history, treatment and outcome
    • Moser, H.W. (1995). Adrenoleukodystrophy: natural history, treatment and outcome. J. Inherited Metab. Dis. 18: 435-447.
    • (1995) J. Inherited Metab. Dis. , vol.18 , pp. 435-447
    • Moser, H.W.1
  • 4
    • 0030860131 scopus 로고    scopus 로고
    • Adrenoleukodystrophy: Phenotype, genetics, pathogenesis and therapy
    • Moser, H.W. (1997). Adrenoleukodystrophy: phenotype, genetics, pathogenesis and therapy. Brain 120: 1485-1508.
    • (1997) Brain , vol.120 , pp. 1485-1508
    • Moser, H.W.1
  • 10
    • 0029913006 scopus 로고    scopus 로고
    • Glycerol trioleato/glycerol trierucate therapy in X-linked adrenoleukodystrophy: Saturated and unsaturated fatty acids in blood cells. Implications for the follow-up
    • Ruiz, M., Pampols, T. and Girós, M. (1996). Glycerol trioleato/glycerol trierucate therapy in X-linked adrenoleukodystrophy: Saturated and unsaturated fatty acids in blood cells. Implications for the follow-up. J. Inherited Metab. Dis. 19: 188-192.
    • (1996) J. Inherited Metab. Dis. , vol.19 , pp. 188-192
    • Ruiz, M.1    Pampols, T.2    Girós, M.3
  • 11
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    • Localization of neuronic acid beta-oxidation in human and rodent peroxisomes. Impaired oxidation in Zellweger syndrome and X-linked adrenoleukodystrophy
    • Sandhir, R., Kahn, M., Chahal, A. and Singh, I. (1998). Localization of neuronic acid beta-oxidation in human and rodent peroxisomes. Impaired oxidation in Zellweger syndrome and X-linked adrenoleukodystrophy. J. Lipid Res. 39: 2161-2171.
    • (1998) J. Lipid Res. , vol.39 , pp. 2161-2171
    • Sandhir, R.1    Kahn, M.2    Chahal, A.3    Singh, I.4
  • 13
    • 0032562653 scopus 로고    scopus 로고
    • Lovastatin and sodium phenylacetate normalize the levels of very long chain fatty acids in skin fibroblasts of X-adrenoleukodystrophy
    • Singh, I., Pahad, K. and Khan, M. (1998). Lovastatin and sodium phenylacetate normalize the levels of very long chain fatty acids in skin fibroblasts of X-adrenoleukodystrophy. FEBS Lett. 426: 342-346.
    • (1998) FEBS Lett. , vol.426 , pp. 342-346
    • Singh, I.1    Pahad, K.2    Khan, M.3
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    • Adrenoleukodystrophy protein enhances association of very-long acyl-coenzyme A synthetase with the peroxisome
    • Yamada, T., Taniwaki, T., Shinnoh, N., Uchiyama, A., Shimozawa, N., Ohyagi, Y., Asahara, H. and Kira, J. (1999). Adrenoleukodystrophy protein enhances association of very-long acyl-coenzyme A synthetase with the peroxisome. Neurology 52: 614-616.
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* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.