Prions, peptides and protein misfolding

Molecular Medicine Today

Volumn 6, Issue 7, 2000, Pages 292-293

  Cohen, Fred E ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

PRION PROTEIN;

AMINO ACID SEQUENCE; BOVINE SPONGIFORM ENCEPHALOPATHY; CREUTZFELDT JAKOB DISEASE; GERSTMANN STRAUSSLER SCHEINKER SYNDROME; HUMAN; NONHUMAN; PRION DISEASE; PROTEIN CONFORMATION; PROTEIN FOLDING; SCRAPIE; SHORT SURVEY; TRANSGENIC MOUSE;

BOVINAE; MUS MUSCULUS;

EID: 0033946710     PISSN: 13574310     EISSN: None     Source Type: Journal    
DOI: 10.1016/S1357-4310(00)01740-8     Document Type: Review

References (9)

1. Cohen F.E., Prusiner S.B. Pathologic conformations of prion proteins. Annu. Rev. Biochem. 67:1998;793-819.
2. Gajdusek D.C., Gibbs C.J. Jr. Transmission of kuru from man to rhesus monkey (Macaca mulatta) 8 and one-half years after inoculation. Nature. 240:1972;351-353.
3. Hill A.F.et al. The same prion strain causes vCJD and BSE. Nature. 389:1997;448-450.
4. Bruce M.E.et al. Transmissions to mice indicate that 'new variant' CJD is caused by the BSE Agent. Nature. 389:1997;498-501.
5. Scott M.R.et al. Compelling transgenetic evidence for transmission of bovine spongiform encephalopathy prions to humans. Proc. Natl. Acad. Sci. U. S. A. 96:1999;15137-15142.
6. Telling G.C.et al. Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity. Science. 274:1996;2079-2082.
7. Supattapone S.et al. Prion protein of 106 residues creates an artificial transmission barrier for prion replication in transgenic mice. Cell. 96:1999;869-878.
8. Kaneko K.et al. A synthetic peptide initiates Gerstmann-Straussler-Scheinker (GSS) disease in transgenic mice. J. Molec. Biol. 295:2000;997-1008.
9. Hsaio K.K.et al. Serial transmission in rodents of neurodegeneration from transgenic nice expressing mutant prion protein. Proc. Natl. Acad. Sci. U. S. A. 91:1994;9126-9130.