Mannose supplementation corrects GDP-mannose deficiency in cultured fibroblasts from some patients with congenital disorders of glycosylation (CDG)

Glycobiology

Volumn 10, Issue 8, 2000, Pages 829-835

  Rush, Jeffrey S ^a   Panneerselvam, K ^b,c   Waechter, Charles J ^a   Freeze, Hudson H ^b  

^a UNIVERSITY OF KENTUCKY MEDICAL CENTER   (United States)

^b BURNHAM INSTITUTE   (United States)

^c University of California at San Diego   (United States)

Author keywords

Congenital disorders of glycosylation (CDG); Fibroblast; GDP mannose; Mannose; Phosphomannose isomerase

Indexed keywords

DOLICHOL PHOSPHATE MANNOSE; GUANOSINE DIPHOSPHATE MANNOSE; MANNOSE; MANNOSE PHOSPHATE ISOMERASE; PHOSPHOMANNOMUTASE; SYNTHETASE;

ARTICLE; BIOSYNTHESIS; CELL LABELING; CELL LEVEL; CONGENITAL DISORDER; CONTROLLED STUDY; CULTURE MEDIUM; FIBROBLAST CULTURE; HUMAN; HUMAN CELL; PRIORITY JOURNAL; PROTEIN GLYCOSYLATION; SUPPLEMENTATION;

EID: 0033890977     PISSN: 09596658     EISSN: None     Source Type: Journal    
DOI: 10.1093/glycob/10.8.829     Document Type: Article

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