Mannose corrects altered N-glycosylation in carbohydrate-deficient glycoprotein syndrome fibroblasts

Journal of Clinical Investigation

Volumn 97, Issue 6, 1996, Pages 1478-1487

  Panneerselvam, K ^a   Freeze, Hudson H ^a  

^a BURNHAM INSTITUTE   (United States)

Author keywords

CDG syndrome; glycoprotein; glycosylation; hexose transporter; lipid linked oligosaccharide

Indexed keywords

ASPARAGINE LINKED OLIGOSACCHARIDE; CONCANAVALIN A; DEOXYGLUCOSE; GLUCOSE TRANSPORTER; GLYCOPROTEIN; GUANOSINE DIPHOSPHATE MANNOSE; MANNOSE; MANNOSE 6 PHOSPHATE; MANNOSE PHOSPHATE; METHIONINE; SULFUR 35; TRITIUM;

ARTICLE; BIOSYNTHESIS; CONGENITAL DISORDER OF GLYCOSYLATION; CONTROLLED STUDY; FIBROBLAST; GLYCOSYLATION; HUMAN; HUMAN CELL; ISOTOPE LABELING; PRIORITY JOURNAL; PROTEIN BINDING;

EID: 0029984537     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI118570     Document Type: Article

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