Carbohydrate-deficient glycoprotein syndrome type 1: Correction of the glycosylation defect by deprivation of glucose or supplementation of mannose

Glycoconjugate Journal

Volumn 15, Issue 5, 1998, Pages 499-505

  Körner, Christian ^a   Lehle, Ludwig ^b   Von Figura, Kurt ^a  

^a UNIVERSITY OF GÖTTINGEN   (Germany)

^b UNIVERSITY OF REGENSBURG   (Germany)

Author keywords

CDGS type 1; Glucose deprivation; Mannose addition

Indexed keywords

GLUCOSE; GLYCOPROTEIN; MANNOSE; MUTASE; OLIGOSACCHARIDE;

ARTICLE; CONGENITAL DISORDER OF GLYCOSYLATION; ENZYME DEFICIENCY; FIBROBLAST CULTURE; GLYCOSYLATION; HUMAN; HUMAN CELL; PRIORITY JOURNAL; STARVATION; SUPPLEMENTATION;

CARBOHYDRATE-DEFICIENT GLYCOPROTEIN SYNDROME; CELLS, CULTURED; FIBROBLASTS; GLUCOSE; GLYCOSYLATION; HUMANS; MANNOSE; PHOSPHOTRANSFERASES (PHOSPHOMUTASES); SKIN;

EID: 0031831143     PISSN: 02820080     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1006939104442     Document Type: Article

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