Ceramide accumulation is associated with increased apoptotic cell death in cultured fibroblasts of sphingolipid activator protein-deficient mouse but not in fibroblasts of patients with Farber disease

Journal of Inherited Metabolic Disease

Volumn 22, Issue 5, 1999, Pages 649-662

  Tohyama, J ^a   Oya, Y ^a,c   Ezoe, T ^a   Vanier, M T ^b   Nakayasu, H ^a,d   Fujita, N ^a,e   Suzuki, K ^a  

^a UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

^b INSERM   (France)

^c UNIVERSITY OF TOKYO   (Japan)

^d TOTTORI UNIVERSITY   (Japan)

^e NIIGATA UNIVERSITY   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

ACYLSPHINGOSINE DEACYLASE; CERAMIDE; SPHINGOLIPID ACTIVATOR PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; APOPTOSIS; ARTICLE; CASE REPORT; CELL DEATH; CONTROLLED STUDY; DNA SYNTHESIS; ENZYME DEFICIENCY; FARBER DISEASE; FIBROBLAST; FIBROBLAST CULTURE; HUMAN; HUMAN CELL; MOUSE; NONHUMAN; NORMAL HUMAN; PROTEIN DEFICIENCY;

AMIDOHYDROLASES; ANIMALS; APOPTOSIS; BRAIN; CELLS, CULTURED; CERAMIDES; FIBROBLASTS; GLYCOPROTEINS; HUMANS; MICE; MICE, KNOCKOUT; SAPOSINS; SPHINGOLIPID ACTIVATOR PROTEINS; SPINAL CORD;

EID: 0033001660     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1005590316064     Document Type: Article

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