The glycosphingolipidoses - From disease to basic principles of metabolism

Biological Chemistry

Volumn 380, Issue 7-8, 1999, Pages 759-766

  Schuette, Christina G ^a   Doering, Thomas ^a   Kolter, Thomas ^a   Sandhoff, Konrad ^a  

^a UNIVERSITY OF BONN   (Germany)

Author keywords

Glycosidase; Glycosphingolipid degradation; Lysosomal storage disease; Skin; Sphingolipid activator protein; Therapy

Indexed keywords

GLYCOLIPID; GLYCOSIDASE; GLYCOSPHINGOLIPID;

CELL MEMBRANE; DEGRADATION; DEVELOPMENT; ENZYME ACTIVITY; HUMAN; LIPID METABOLISM; LYSOSOME STORAGE DISEASE; PRIORITY JOURNAL; REVIEW; SKIN;

ANIMALS; CARBOHYDRATE SEQUENCE; EPIDERMIS; GLYCOSPHINGOLIPIDS; HUMANS; LYSOSOMAL STORAGE DISEASES; LYSOSOMES; MICE; MOLECULAR SEQUENCE DATA;

EID: 0032853773     PISSN: 14316730     EISSN: None     Source Type: Journal    
DOI: 10.1515/BC.1999.096     Document Type: Review

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