α-Mannosidosis in the guinea pig: A new animal model for lysosomal storage disorders

Pediatric Research

Volumn 46, Issue 5, 1999, Pages 501-509

  Crawley, Allison C ^a,e   Jones, Margaret Z ^b   Bonning, Lynda E ^d   Finnie, John W ^c   Hopwood, John J ^a  

^a WOMEN S AND CHILDREN S HOSPITAL   (Australia)

^b MICHIGAN STATE UNIVERSITY   (United States)

^c INSTITUTE OF MEDICAL AND VETERINARY SCIENCE   (Australia)

^d Canterbury Veterinary Clinic   (Australia)

^e Department of Chemical Pathology ^*  (Australia)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA LEVO FUCOSIDASE; ALPHA MANNOSIDASE; ALPHA N ACETYLGALACTOSAMINIDASE; BETA GALACTOSIDASE; BETA GLUCURONIDASE; BETA MANNOSIDASE; BETA N ACETYLHEXOSAMINIDASE A; OLIGOSACCHARIDE;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BODY POSTURE; CELL VACUOLE; CENTRAL NERVOUS SYSTEM; CONTROLLED STUDY; GAIT; GUINEA PIG; LEUKOCYTE; LIVER HOMOGENATE; LYSOSOME STORAGE DISEASE; MALE; MANNOSIDOSIS; MENTAL DETERIORATION; NONHUMAN; PRIORITY JOURNAL; SKIN FIBROBLAST; THIN LAYER CHROMATOGRAPHY;

EID: 0032744328     PISSN: 00313998     EISSN: None     Source Type: Journal    
DOI: 10.1203/00006450-199911000-00003     Document Type: Article

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