Genetic diseases of the extracellular matrix: More than just connective tissue disorders

Journal of Molecular Medicine

Volumn 76, Issue 3-4, 1998, Pages 226-237

  Bruckner Tuderman, Leena ^a,b   Bruckner, Peter ^b,c  

^a UNIVERSITY OF OULU   (Finland)

^b UNIVERSITY OF MÜNSTER   (Germany)

^c UNIVERSITY OF BASEL   (Switzerland)

Author keywords

Collagens; Development; Gene defects; Laminins; Mutatins; Patterning; Proteoglycans; Receptors

Indexed keywords

CALCIUM BINDING PROTEIN; COLLAGEN; COLLAGEN FIBRIL; COLLAGEN TYPE 1; COLLAGEN TYPE 10; COLLAGEN TYPE 2; COLLAGEN TYPE 3; COLLAGEN TYPE 4; COLLAGEN TYPE 5; COLLAGEN TYPE 6; COLLAGEN TYPE 7; COLLAGEN TYPE 8; CYTOSKELETON PROTEIN; DYSTROPHIN; ELASTIN; FIBRILLIN; FIBROBLAST GROWTH FACTOR; GROWTH FACTOR RECEPTOR; INTEGRIN; KALININ; LAMININ; MATRIX PROTEIN; MEROSIN; PARATHYROID HORMONE; PROCOLLAGEN; PROTEOGLYCAN; RECEPTOR; STRUCTURAL PROTEIN; THROMBOSPONDIN;

COLLAGEN DISEASE; CONNECTIVE TISSUE DISEASE; DEVELOPMENTAL DISORDER; EXTRACELLULAR MATRIX; GENETIC DISORDER; HUMAN; MUSCULAR DYSTROPHY; MUTATION; PHENOTYPE; PROTEIN SYNTHESIS; REVIEW; SIGNAL TRANSDUCTION;

CONNECTIVE TISSUE DISEASES; EXTRACELLULAR MATRIX; EXTRACELLULAR MATRIX PROTEINS; HUMANS;

EID: 0031933384     PISSN: 09462716     EISSN: None     Source Type: Journal    
DOI: 10.1007/s001090050213     Document Type: Review

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