Mice deficient in all forms of lysosomal β-hexosaminidase show mucopolysaccharidosis-like pathology

Journal of Neuropathology and Experimental Neurology

Volumn 56, Issue 6, 1997, Pages 693-703

  Suzuki, Kinuko ^a,b   Sango, Kazunori ^a,b   Proia, Richard L ^b   Langaman, Clarita ^a  

^a UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

^b NATIONAL INSTITUTE OF DIABETES AND DIGESTIVE AND KIDNEY DISEASES   (United States)

Author keywords

Glycosaminoglycans; GM2 gangliosidosis; Hypomyelination; Knockout mice; Microglia; Mucopolysaccharidosis

Indexed keywords

BETA N ACETYLHEXOSAMINIDASE; GANGLIOSIDE GM2; GLYCOSAMINOGLYCAN; LYSOSOME ENZYME;

ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; DEGENERATIVE DISEASE; ELECTRON MICROSCOPY; ENZYME DEFICIENCY; ENZYME SUBUNIT; FEMALE; GANGLIOSIDOSIS; GENE MUTATION; LYSOSOME STORAGE DISEASE; MALE; MICROGLIA; MOUSE; NEUROPATHOLOGY; NONHUMAN; PRIORITY JOURNAL;

EID: 0030833982     PISSN: 00223069     EISSN: None     Source Type: Journal    
DOI: 10.1097/00005072-199706000-00007     Document Type: Article

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