Myoclonic epilepsy and ragged red fibers (MERRF) syndrome: Selective vulnerability of CNS neurons does not correlate with the level of mitochondrial tRNA(lys) mutation in individual neuronal isolates

Journal of Neuroscience

Volumn 17, Issue 20, 1997, Pages 7746-7753

  Zhou, Li ^a   Chomyn, Anne ^b   Attardi, Giuseppe ^b   Miller, Carol A ^a  

^a UNIVERSITY OF SOUTHERN CALIFORNIA   (United States)

^b CALIFORNIA INSTITUTE OF TECHNOLOGY   (United States)

Author keywords

CNS microdissection; MERRF syndrome; mtDNA; Neurodegeneration; PCR; tRNA(Lys)

Indexed keywords

ARTICLE; CELL ISOLATION; CELL SUBPOPULATION; GENE AMPLIFICATION; GENE MUTATION; GENOTYPE; HUMAN; HUMAN CELL; HUMAN TISSUE; MERRF SYNDROME; MYOCLONUS EPILEPSY; NERVE DEGENERATION; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL;

EID: 0030826380     PISSN: 02706474     EISSN: None     Source Type: Journal    
DOI: 10.1523/jneurosci.17-20-07746.1997     Document Type: Article

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