Phytanic acid α-oxidation: Decarboxylation of 2-hydroxyphytanoyl-CoA to pristanic acid in human liver

Journal of Lipid Research

Volumn 38, Issue 10, 1997, Pages 2062-2070

  Verhoeven, Nanda M ^a   Wanders, Ronald J A ^b   Schor, Danielle S M ^a   Jansen, Gerbert A ^b   Jakobs, Cornelis ^a  

^a VU UNIVERSITY AMSTERDAM   (Netherlands)

^b ACADEMIC MEDICAL CENTER   (Netherlands)

Author keywords

Gas chromatography mass spectometry; Microsome; Peroxisome

Indexed keywords

2 HYDROXYPHYTANIC ACID; 2 HYDROXYPHYTANOYL COENZYME A; ADENOSINE TRIPHOSPHATE; COENZYME A; FATTY ACID DERIVATIVE; MAGNESIUM ION; NICOTINAMIDE ADENINE DINUCLEOTIDE; NICOTINAMIDE ADENINE DINUCLEOTIDE PHOSPHATE; PHYTANIC ACID; PRISTANIC ACID; UNCLASSIFIED DRUG;

ARTICLE; CONTROLLED STUDY; DECARBOXYLATION; FATTY ACID METABOLISM; FATTY ACID OXIDATION; HUMAN; HUMAN TISSUE; LIVER HOMOGENATE; LIVER MICROSOME; PRIORITY JOURNAL; ZELLWEGER SYNDROME;

BIOLOGICAL MARKERS; CELL FRACTIONATION; COENZYME A; DECARBOXYLATION; FATTY ACIDS; HUMANS; LIVER; MICROBODIES; MICROSOMES; NAD; PHYTANIC ACID; ZELLWEGER SYNDROME;

EID: 0030725292     PISSN: 00222275     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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