Dissociation between the level of von Willebrand factor-cleaving protease activity and disease in a patient with congenital thrombotic thrombocytopenic purpura

American Journal of Hematology

Volumn 77, Issue 4, 2004, Pages 387-390

  Snider, Carolyn E ^a   Moore, Jane C ^a   Warkentin, Theodore E ^a   Finch, Clara N ^a   Hayward, Catherine P M ^a   Kelton, John G ^a  

^a MCMASTER UNIVERSITY   (Canada)

Author keywords

ADAMTS13 activity; Congenital TTP; Splenectomy

Indexed keywords

DNA; FRESH FROZEN PLASMA; VON WILLEBRAND FACTOR; VON WILLEBRAND FACTOR CLEAVING PROTEINASE;

ADAMTS13 GENE; ADULT; APHASIA; ARTICLE; CASE REPORT; CEREBROVASCULAR ACCIDENT; DNA DETERMINATION; ENZYME ACTIVITY; FEMALE; GENE; HEMODIALYSIS; HEMOLYTIC ANEMIA; HOMOZYGOSITY; HUMAN; HUMAN CELL; KIDNEY FAILURE; LONGITUDINAL STUDY; PLASMAPHERESIS; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; REMISSION; SPLENECTOMY; THROMBOCYTE COUNT; THROMBOTIC THROMBOCYTOPENIC PURPURA; TRANSIENT ISCHEMIC ATTACK; UPSHAW SCHULMAN SYNDROME;

EID: 9644266966     PISSN: 03618609     EISSN: None     Source Type: Journal    
DOI: 10.1002/ajh.20221     Document Type: Article

References (14)

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