Radiological pleuroparenchymal fibroelastosis associated to limited cutaneous systemic sclerosis: A case report

BMC Pulmonary Medicine

Volumn 18, Issue 1, 2018, Pages

  Hassoun, D ^a   Dirou, S ^b   Arrigoni, P P ^a   Durant, C ^a   Hamidou, M ^a   Neel A ^a   Agard, C ^a  

^a HÔTEL DIEU   (France)

^b CHU de Nantes   (France)

Author keywords

Interstitial lung disease; Pleuroparenchymal fibroelastosis; Systemic sclerosis

Indexed keywords

CENTROMERE ANTIBODY; FLUORODEOXYGLUCOSE F 18; TELOMERASE; TELOMERASE REVERSE TRANSCRIPTASE; ANTINUCLEAR ANTIBODY;

ADULT; ARTICLE; CASE REPORT; CAUCASIAN; CLINICAL ARTICLE; COMPUTER ASSISTED TOMOGRAPHY; DISEASE ASSOCIATION; ECHOCARDIOGRAPHY; FEMALE; FOLLOW UP; GENE; GENE MUTATION; HUMAN; INTERSTITIAL LUNG DISEASE; LUNG FUNCTION TEST; MIDDLE AGED; PLEURA THICKENING; PLEUROPARENCHYMAL FIBROELASTOSIS; POSITRON EMISSION TOMOGRAPHY; PROGNOSIS; SEQUENCE ANALYSIS; SYSTEMIC SCLEROSIS; TERC GENE; TERT GENE; THROMBOCYTOPENIA; TOTAL LUNG CAPACITY; BLOOD; DIAGNOSTIC IMAGING; DISEASE EXACERBATION; IMMUNOLOGY; LIMITED SCLERODERMA; PARENCHYMA; PATHOLOGY; PATHOPHYSIOLOGY; PLEURA; PLEURA DISEASE; PROCEDURES; X-RAY COMPUTED TOMOGRAPHY;

ANTIBODIES, ANTINUCLEAR; DISEASE PROGRESSION; FEMALE; HUMANS; LUNG DISEASES, INTERSTITIAL; MIDDLE AGED; PARENCHYMAL TISSUE; PLEURA; PLEURAL DISEASES; RESPIRATORY FUNCTION TESTS; SCLERODERMA, LIMITED; SCLERODERMA, SYSTEMIC; TOMOGRAPHY, X-RAY COMPUTED;

EID: 85047090949     PISSN: None     EISSN: 14712466     Source Type: Journal    
DOI: 10.1186/s12890-018-0641-5     Document Type: Article

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