Pleuroparenchymal fibroelastosis: A spectrum of histopathological and imaging phenotypes

European Respiratory Journal

Volumn 40, Issue 2, 2012, Pages 377-385

  Reddy, Taryn L ^a   Tominaga, Masaki ^b   Hansell, David M ^a   Von Der Thusen, Jan ^b   Rassl, Doris ^c   Parfrey, Helen ^d   Guy, Suzy ^e   Twentyman, Orion ^f   Rice, Alexandra ^b   Maher, Toby M ^a   Renzoni, Elisabetta A ^a   Wells, Athol U ^a   Nicholson, Andrew G ^a  

^a IMPERIAL COLLEGE LONDON   (United Kingdom)

^b ROYAL BROMPTON AND HAREFIELD NHS FOUNDATION TRUST   (United Kingdom)

^c UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^d UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^e ROYAL GROUP OF HOSPITALS TRUST   (United Kingdom)

^f NORFOLK AND NORWICH UNIVERSITY HOSPITAL   (United Kingdom)

Author keywords

Infection; Interstitial lung disease; Lung; Pleuropulmonary fibroelastosis

Indexed keywords

ACETYLCYSTEINE; ANTIFUNGAL AGENT; AUTOANTIBODY; AZATHIOPRINE; AZITHROMYCIN; CYCLOPHOSPHAMIDE; MEPREDNISONE; PREDNISONE;

ADULT; AGED; ALLERGIC BRONCHOPULMONARY ASPERGILLOSIS; ALLERGIC PNEUMONITIS; BRONCHIECTASIS; CLINICAL ARTICLE; CLINICAL FEATURE; COUGHING; DRUG MEGADOSE; DRUG RESPONSE; DYSPNEA; FAMILY HISTORY; FEMALE; HIGH RESOLUTION COMPUTER TOMOGRAPHY; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; INTERSTITIAL LUNG DISEASE; INTERSTITIAL PNEUMONIA; LOW DRUG DOSE; LUNG BIOPSY; LUNG FIBROSIS; MALE; PHENOTYPE; PLEURA DISEASE; PLEUROPARENCHYMAL FIBROELASTOSIS; PRIORITY JOURNAL; RECURRENT INFECTION; REVIEW;

ADULT; AGED; AGED, 80 AND OVER; BIOPSY; COUGH; DYSPNEA; FEMALE; HUMANS; LUNG; LUNG DISEASES, INTERSTITIAL; MALE; MIDDLE AGED; PHENOTYPE; PLEURA; PULMONARY ALVEOLI; PULMONARY FIBROSIS; TOMOGRAPHY, X-RAY COMPUTED; TREATMENT OUTCOME;

EID: 84864743454     PISSN: 09031936     EISSN: 13993003     Source Type: Journal    
DOI: 10.1183/09031936.00165111     Document Type: Review

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