Degree of Cajal–Retzius Cell Mislocalization Correlates with the Severity of Structural Brain Defects in Mouse Models of Dystroglycanopathy

Brain Pathology

Volumn 26, Issue 4, 2016, Pages 465-478

  Booler, Helen S ^a   Williams, Josie L ^a   Hopkinson, Mark ^a   Brown, Susan C ^a  

^a ROYAL VETERINARY COLLEGE   (United Kingdom)

Author keywords

Cajal Retzius cells; congenital muscular dystrophy; dystroglycan; neuronal migration; pial basement membrane; reelin

Indexed keywords

ALPHA DYSTROGLYCAN; CELL SURFACE RECEPTOR;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN CELL; BRAIN DAMAGE; CAJAL RETZIUS CELL; DAG1 GENE; DISEASE SEVERITY; DYSTROGLYCANOPATHY; EXON; FKRP GENE; GENE; GENE DELETION; GENE MUTATION; LARGE GENE; MOUSE; NEUROMUSCULAR DISEASE; NONHUMAN; PATHOGENESIS; PHENOTYPE; POMGNT1 GENE; PROTEIN GLYCOSYLATION;

EID: 85027943172     PISSN: 10156305     EISSN: 17503639     Source Type: Journal    
DOI: 10.1111/bpa.12306     Document Type: Article

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