Thalassemias in South Asia: clinical lessons learnt from Bangladesh

Orphanet Journal of Rare Diseases

Volumn 12, Issue 1, 2017, Pages

  Hossain, Mohammad Sorowar ^a,b,c   Raheem, Enayetur ^a   Sultana, Tanvira Afroze ^a   Ferdous, Shameema ^a   Nahar, Nusrat ^d   Islam, Sazia ^e   Arifuzzaman, Mohammad ^a   Razzaque, Mohammad Abdur ^a,e   Alam, Rabiul ^a   Aziz, Sonia ^f   Khatun, Hazera ^g   Rahim, Abdur ^d   Morshed, Manzur ^d  

^a Biomedical Research Foundation   (Bangladesh)

^b BANGLADESH UNIVERSITY OF HEALTH SCIENCES   (Bangladesh)

^c INDEPENDENT UNIVERSITY   (Bangladesh)

^d Thalassemia Foundation Hospital   (Bangladesh)

^e TRINITY COLLEGE DUBLIN   (Ireland)

^f MORAVIAN COLLEGE   (United States)

^g ST MICHAEL S MEDICAL CENTER   (United States)

Author keywords

Bangladesh; Beta thalassemia; Beta thalassemia major; HbE beta thalassemia; Hemoglobinopathies; Non transfusion dependent thalassemia; Thalassemia trait; Transfusion dependent thalassemia

Indexed keywords

DEFERASIROX; DEFEROXAMINE MESYLATE; HYDROXYUREA; IRON CHELATING AGENT;

BANGLADESH; BLOOD TRANSFUSION; CHILDHOOD MORTALITY; CLINICAL OUTCOME; CLINICAL PRACTICE; COUNSELING; DEVELOPING COUNTRY; DISEASE COURSE; GENE MUTATION; HEALTH CARE COST; HUMAN; IRON CHELATION; MARRIAGE; PRENATAL SCREENING; PREVALENCE; PREVENTIVE MEDICINE; PUBLIC HEALTH PROBLEM; PUBLIC HEALTH SERVICE; REVIEW; THALASSEMIA; TREATMENT RESPONSE; ANIMAL; ASIA; BETA THALASSEMIA; GENETICS; HEMOGLOBINOPATHY; METABOLISM; MUTATION;

ANIMALS; ASIA; BANGLADESH; BETA-THALASSEMIA; HEMOGLOBINOPATHIES; HUMANS; MUTATION; THALASSEMIA;

EID: 85019638263     PISSN: None     EISSN: 17501172     Source Type: Journal    
DOI: 10.1186/s13023-017-0643-z     Document Type: Review

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