Cardiac phenotype and long-term prognosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia patients with late presentation

Heart Rhythm

Volumn 14, Issue 6, 2017, Pages 883-891

  Bhonsale, Aditya ^a   te Riele, Anneline S J M ^b   Sawant, Abhishek C ^a   Groeneweg, Judith A ^b   James, Cynthia A ^a   Murray, Brittney ^a   Tichnell, Crystal ^a   Mast, Thomas P ^b   van der Pols, Michelle J ^b   Cramer, Maarten J M ^b   Dooijes, Dennis ^b   van der Heijden, Jeroen F ^b   Tandri, Harikrishna ^a   van Tintelen, J Peter ^c,d   Judge, Daniel P ^a   Hauer, Richard N W ^d   Calkins, Hugh ^a  

^a JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^c ACADEMIC MEDICAL CENTER   (Netherlands)

^d INTERUNIVERSITY CARDIOLOGY INSTITUTE OF THE NETHERLANDS   (Netherlands)

Author keywords

Arrhythmogenic right ventricular cardiomyopathy dysplasia; Cardiomyopathy; Genotype; Late onset; Outcome

Indexed keywords

ANTIARRHYTHMIC AGENT; DESMOGLEIN 2; DESMOPLAKIN; PHOSPHOLAMBAN; PLAKOPHILIN 2; UNCLASSIFIED DRUG; PKP2 PROTEIN, HUMAN; PLAKOPHILIN;

AGED; ARTICLE; ATRIAL FIBRILLATION; CARDIOVASCULAR MAGNETIC RESONANCE; CLINICAL OUTCOME; DRUG USE; ELECTROCARDIOGRAM; FAINTNESS; FAMILY HISTORY; FEMALE; FOLLOW UP; GENE MUTATION; GENOTYPE; HEART ARRHYTHMIA; HEART ATRIUM FLUTTER; HEART DEATH; HEART FAILURE; HEART LEFT VENTRICLE FAILURE; HEART REPOLARIZATION; HEART RIGHT VENTRICLE DYSPLASIA; HEART TRANSPLANTATION; HEART VENTRICLE TACHYCARDIA; HOLTER MONITORING; HUMAN; IMPLANTABLE CARDIOVERTER DEFIBRILLATOR; MAJOR CLINICAL STUDY; MALE; PHENOTYPE; PRIMARY PREVENTION; PRIORITY JOURNAL; PROGNOSIS; SUDDEN CARDIAC DEATH; T WAVE; T WAVE INVERSION; ADOLESCENT; ADULT; CLINICAL TRIAL; ELECTROCARDIOGRAPHY; GENETIC PREDISPOSITION; GENETICS; INCIDENCE; METABOLISM; MIDDLE AGED; MULTICENTER STUDY; PATHOPHYSIOLOGY; RETROSPECTIVE STUDY; RISK ASSESSMENT; SURVIVAL RATE; TIME FACTOR; TRENDS; UNITED STATES; YOUNG ADULT;

ADOLESCENT; ADULT; ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA; ELECTROCARDIOGRAPHY; FEMALE; FOLLOW-UP STUDIES; GENETIC PREDISPOSITION TO DISEASE; GENOTYPE; HUMANS; INCIDENCE; MALE; MIDDLE AGED; PHENOTYPE; PLAKOPHILINS; PROGNOSIS; RETROSPECTIVE STUDIES; RISK ASSESSMENT; SURVIVAL RATE; TIME FACTORS; UNITED STATES; YOUNG ADULT;

EID: 85018908978     PISSN: 15475271     EISSN: 15563871     Source Type: Journal    
DOI: 10.1016/j.hrthm.2017.02.013     Document Type: Article

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