Arrhythmogenic right ventricular cardiomyopathy/dysplasia on the basis of the revised diagnostic criteria in affected families with desmosomal mutations

European Heart Journal

Volumn 32, Issue 9, 2011, Pages 1097-1104

  Protonotarios, Nikos ^a   Anastasakis, Aris ^b   Antoniades, Loizos ^c   Chlouverakis, Gregory ^d   Syrris, Petros ^e   Basso, Cristina ^f   Asimaki, Angeliki ^e   Theopistou, Artemisia ^b   Stefanadis, Christodoulos ^b   Thiene, Gaetano ^f   McKenna, William J ^e   Tsatsopoulou, Adalena ^a  

^a Yannis Protonotarios Medical Centre   (Greece)

^b UNIVERSITY OF ATHENS MEDICAL SCHOOL   (Greece)

^c Larnaca General Hospital   (Cyprus)

^d UNIVERSITY OF CRETE   (Greece)

^e UNIVERSITY COLLEGE LONDON   (United Kingdom)

^f UNIVERSITY OF PADUA MEDICAL SCHOOL   (Italy)

Author keywords

Arrhythmogenic right ventricular cardiomyopathy dysplasia; Cardiomyopathy; Desmosome mutations; Diagnostic criteria

Indexed keywords

ADULT; ARTICLE; CLINICAL ASSESSMENT; CLINICAL ASSESSMENT TOOL; CONTROLLED STUDY; DESMOSOME; DOMINANT INHERITANCE; ECG ABNORMALITY; ELECTROCARDIOGRAPHY; EVENT FREE SURVIVAL; FAMILIAL DISEASE; FEMALE; GENE MUTATION; HEART RIGHT VENTRICLE DYSPLASIA; HEART VENTRICLE ARRHYTHMIA; HETEROZYGOTE; HUMAN; MAJOR CLINICAL STUDY; MALE; PENETRANCE; PRIORITY JOURNAL; PROSPECTIVE STUDY; RECESSIVE INHERITANCE; SENSITIVITY AND SPECIFICITY; TASK FORCE CRITERIA; TWO DIMENSIONAL ECHOCARDIOGRAPHY; ADOLESCENT; AGED; ECHOCARDIOGRAPHY; GENETICS; HEART ARRHYTHMIA; HOMOZYGOTE; KAPLAN MEIER METHOD; MIDDLE AGED; MUTATION; PEDIGREE;

ADOLESCENT; ADULT; AGED; AGED, 80 AND OVER; ARRHYTHMIAS, CARDIAC; ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA; DESMOSOMES; ECHOCARDIOGRAPHY; ELECTROCARDIOGRAPHY, AMBULATORY; FEMALE; HETEROZYGOTE; HOMOZYGOTE; HUMANS; KAPLAN-MEIER ESTIMATE; MALE; MIDDLE AGED; MUTATION; PEDIGREE; PROSPECTIVE STUDIES; YOUNG ADULT;

EID: 80655136498     PISSN: 0195668X     EISSN: 15229645     Source Type: Journal    
DOI: 10.1093/eurheartj/ehr043     Document Type: Article

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