Incidence and predictors of sudden death, major conduction defects and sustained ventricular tachyarrhythmias in 1388 patients withmyotonic dystrophy type 1

European Heart Journal

Volumn 38, Issue 10, 2017, Pages 751-758

  Wahbi, Karim ^a,b,c   Babuty, Dominique ^d   Probst, Vincent ^e   Wissocque, Ludivine ^f   Labombarda, Fabien ^g   Porcher, Raphaël ^h,i,j   Bécane, Henri Marc ^b   Lazarus, Arnaud ^k   Béhin, Anthony ^b   Laforêt, Pascal ^b,l   Stojkovic, Tanya ^b   Clementy, Nicolas ^d   Dussauge, Aurélie Pattier ^e,m   Gourraud, Jean Baptiste ^e   Pereon, Yann ^m   Lacour, Arnaud ^f   Chapon, Françoise ^g   Milliez, Paul ^g   Klug, Didier ^f   Eymard, Bruno ^b,l   Duboc, Denis ^a,b,c   more..

^a Institut Cochin   (France)

^b PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

^c Sorbonne Université   (France)

^d UNIVERSITÉ DE TOURS   (France)

^e INSERM   (France)

^f LILLE UNIVERSITY HOSPITAL   (France)

^g CAEN UNIVERSITY HOSPITAL   (France)

^h PARIS DESCARTES UNIVERSITY   (France)

ⁱ UNIVERSITÉ PARIS DESCARTES   (France)

^j HÔTEL DIEU   (France)

^k In Parys Clinic Research Group   (France)

^l SORBONNE UNIVERSITÉ   (France)

^m NANTES UNIVERSITY HOSPITAL   (France)

more..

Author keywords

Implantable cardioverter defibrillator; Myotonic dystrophy cardiomyopathy; Preventive pacing; Sudden cardiac death; Ventricular tachyarrhythmia; Ventricular tachycardia

Indexed keywords

AMIODARONE; ANGIOTENSIN RECEPTOR ANTAGONIST; BETA ADRENERGIC RECEPTOR BLOCKING AGENT; DIPEPTIDYL CARBOXYPEPTIDASE INHIBITOR;

ADULT; ARTICLE; ATRIAL FIBRILLATION; AUTOPSY; CARDIAC RESYNCHRONIZATION THERAPY; COMPLETE HEART BLOCK; CONTROLLED STUDY; DISEASE ASSOCIATION; ECG ABNORMALITY; ELECTROMECHANICAL DISSOCIATION; FAINTNESS; FEMALE; FIRST DEGREE ATRIOVENTRICULAR BLOCK; FOLLOW UP; FRANCE; HEART ARREST; HEART ARRHYTHMIA; HEART LEFT BUNDLE BRANCH BLOCK; HEART MUSCLE CONDUCTION DISTURBANCE; HEART PACING; HEART RHYTHM; HEART VENTRICLE TACHYCARDIA; HUMAN; INCIDENCE; MAJOR CLINICAL STUDY; MALE; MIDDLE AGED; MULTICENTER STUDY; MYOTONIC DYSTROPHY; OVERALL SURVIVAL; PREDICTOR VARIABLE; PRIORITY JOURNAL; PROPORTIONAL HAZARDS MODEL; SECOND DEGREE ATRIOVENTRICULAR BLOCK; SINUS NODE DISEASE; SUDDEN CARDIAC DEATH; UNIVERSITY HOSPITAL; AGE; ATRIOVENTRICULAR BLOCK; CLINICAL TRIAL; COMPLICATION; HEART BUNDLE BRANCH BLOCK; IMPLANTABLE CARDIOVERTER DEFIBRILLATOR; MORTALITY; PEDIGREE; RETROSPECTIVE STUDY;

ADULT; AGE FACTORS; ATRIOVENTRICULAR BLOCK; BUNDLE-BRANCH BLOCK; CARDIAC CONDUCTION SYSTEM DISEASE; CARDIAC PACING, ARTIFICIAL; DEATH, SUDDEN, CARDIAC; DEFIBRILLATORS, IMPLANTABLE; FEMALE; HUMANS; MALE; MIDDLE AGED; MYOTONIC DYSTROPHY; PEDIGREE; RETROSPECTIVE STUDIES; TACHYCARDIA, VENTRICULAR;

EID: 85016207788     PISSN: 0195668X     EISSN: 15229645     Source Type: Journal    
DOI: 10.1093/eurheartj/ehw569     Document Type: Article

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