High levels of sarcospan are well tolerated and act as a sarcolemmal stabilizer to address skeletal muscle and pulmonary dysfunction in DMD

Human Molecular Genetics

Volumn 25, Issue 24, 2016, Pages 5395-5406

  Gibbs, Elizabeth M ^a   Marshall, Jamie L ^a,c   Ma, Eva ^a   Nguyen, Thien M ^a   Hong, Grace ^a   Lam, Jessica S ^a   Spencer, Melissa J ^a   Crosbie Watson, Rachelle H ^a,b  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c BROAD INSTITUTE OF MIT AND HARVARD   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

MEMBRANE PROTEIN; SARCOSPAN; UNCLASSIFIED DRUG; CARRIER PROTEIN; SSPN PROTEIN, HUMAN; TUMOR PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; DIAPHRAGM; DUCHENNE MUSCULAR DYSTROPHY; EXERCISE; HISTOPATHOLOGY; LUNG FUNCTION; LUNG INSUFFICIENCY; MEMBRANE STABILIZATION; MORTALITY; MOUSE; MUSCLE FATIGUE; MUSCLE FIBER MEMBRANE; MUSCLE WEAKNESS; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; SARCOLEMMA; SKELETAL MUSCLE; ANIMAL; BIOSYNTHESIS; DISEASE MODEL; GENE EXPRESSION REGULATION; GENETICS; HUMAN; LUNG DISEASE; METABOLISM; MUSCLE CONTRACTION; PATHOLOGY; TRANSGENIC MOUSE; X CHROMOSOME LINKED MUSCULAR DYSTROPHIC MOUSE;

ANIMALS; CARRIER PROTEINS; DISEASE MODELS, ANIMAL; GENE EXPRESSION REGULATION; HUMANS; LUNG DISEASES; MEMBRANE PROTEINS; MICE; MICE, INBRED MDX; MICE, TRANSGENIC; MUSCLE CONTRACTION; MUSCLE, SKELETAL; MUSCULAR DYSTROPHY, DUCHENNE; NEOPLASM PROTEINS; SARCOLEMMA;

EID: 85016059997     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddw356     Document Type: Article

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