Mitochondrial DNA disturbances and deregulated expression of oxidative phosphorylation and mitochondrial fusion proteins in sporadic inclusion body myositis

Clinical Science

Volumn 130, Issue 19, 2016, Pages 1741-1751

  Catalán García, Marc ^a,b   Garrabou, Glòria ^a,b   Morén, Constanza ^a,b   Guitart Mampel, Mariona ^a,b   Hernando, Adriana ^a,b   Díaz Ramos, Àngels ^c,d,e   González Casacuberta, Ingrid ^a,b   Juárez, Diana Luz ^a,b   Bañó, Maria ^a,b   Enrich Bengoa, Jennifer ^a,b   Emperador, Sonia ^f   Milisenda, José César ^a,b   Moreno, Pedro ^a,b   Tobías, Ester ^a,b   Zorzano, Antonio ^c,d,e   Montoya, Julio ^f   Cardellach, Francesc ^a,b   Grau, Josep Maria ^a,b  

^a UNIVERSITY OF BARCELONA   (Spain)

^b HOSPITAL CLÍNIC   (Spain)

^c INSTITUTE FOR RESEARCH IN BIOMEDICINE   (Spain)

^d UNIVERSITY OF BARCELONA   (Spain)

^e INSTITUTO DE SALUD CARLOS III   (Spain)

^f UNIVERSITY OF ZARAGOZA   (Spain)

Author keywords

Deletions; Depletion; Mitochondria; Mitofusin 2; OPA1; Sporadic inclusion body myositis

Indexed keywords

HYBRID PROTEIN; MITOCHONDRIAL DNA; MITOCHONDRIAL PROTEIN; MITOFUSIN 2; RNA;

ARTICLE; CLINICAL ARTICLE; CONTROLLED STUDY; ENZYME ACTIVITY; HUMAN; HUMAN CELL; HUMAN TISSUE; INCLUSION BODY MYOSITIS; MITOCHONDRIAL DYNAMICS; MUSCLE; MUSCLE BIOPSY; OXIDATIVE PHOSPHORYLATION; OXIDATIVE STRESS; PERIPHERAL BLOOD MONONUCLEAR CELL; PRIORITY JOURNAL; PROTEIN EXPRESSION; RESPIRATORY CHAIN; AGED; CASE CONTROL STUDY; FEMALE; GENE EXPRESSION REGULATION; GENETICS; MALE; METABOLISM; MIDDLE AGED; MITOCHONDRION; MONONUCLEAR CELL;

AGED; CASE-CONTROL STUDIES; DNA, MITOCHONDRIAL; FEMALE; GENE EXPRESSION REGULATION; HUMANS; LEUKOCYTES, MONONUCLEAR; MALE; MIDDLE AGED; MITOCHONDRIA; MITOCHONDRIAL PROTEINS; MYOSITIS, INCLUSION BODY; OXIDATIVE PHOSPHORYLATION;

EID: 85014130474     PISSN: 01435221     EISSN: 14708736     Source Type: Journal    
DOI: 10.1042/CS20160080     Document Type: Article

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