Physician driven variation in the care of children with spinal muscular atrophy type 1

Pediatric Pulmonology

Volumn 52, Issue 5, 2017, Pages 662-668

  Oskoui, Maryam ^a   Ng, Pamela ^b   Liben, Stephen ^a   Zielinski, David ^a  

^a MCGILL UNIVERSITY   (Canada)

^b RESEARCH INSTITUTE OF THE MCGILL UNIVERSITY HEALTH CENTRE   (Canada)

Author keywords

neuromuscular diseases; quality of life; respiratory support; spinal muscular atrophy

Indexed keywords

ANTIINFLAMMATORY AGENT; DISEASE MODIFYING TREATMENT; UNCLASSIFIED DRUG;

AERATION; ARTICLE; BREATHING EXERCISE; CANADA; CHILD; CHILD CARE; CHRONIC RESPIRATORY FAILURE; CLINICAL PRACTICE; CONTROLLED STUDY; CROSS-SECTIONAL STUDY; ENDOTRACHEAL INTUBATION; FEMALE; GAS EXCHANGE; GAS MASK; HAPPINESS; HEALTH CARE ACCESS; HOSPITALIZATION; HUMAN; HYPOVENTILATION; INTER PHYSICIAN VARIABILITY; LIFE EXPECTANCY; LUNG CLEARANCE; LUNG VOLUME; MAJOR CLINICAL STUDY; MALE; MECHANICAL INSUFFLATION EXSUFFLATION DEVICE; MEDICAL DECISION MAKING; MEDICAL EDUCATION; MEDICAL SPECIALIST; NEUROLOGIST; NONINVASIVE VENTILATION; PALLIATIVE THERAPY; PEDIATRICS; PERCEPTION; PHYSICIAN; POSITIVE END EXPIRATORY PRESSURE; PROPHYLAXIS; QUALITY OF LIFE; QUEBEC; RESPIROLOGIST; SOCIAL SUPPORT; SPINAL MUSCULAR ATROPHY; SPINAL MUSCULAR ATROPHY TYPE 1; SUCTION; TRACHEOSTOMY; TREATMENT DURATION; COMPLICATION; DECISION MAKING; HEALTH CARE SURVEY; PARENT; PATIENT PARTICIPATION; PRESCHOOL CHILD; RESPIRATORY INSUFFICIENCY; SPINAL MUSCULAR ATROPHIES OF CHILDHOOD;

CANADA; CHILD; CHILD, PRESCHOOL; CROSS-SECTIONAL STUDIES; DECISION MAKING; FEMALE; HEALTH CARE SURVEYS; HUMANS; MALE; NONINVASIVE VENTILATION; PARENTS; PATIENT PARTICIPATION; RESPIRATORY INSUFFICIENCY; SPINAL MUSCULAR ATROPHIES OF CHILDHOOD; TRACHEOSTOMY;

EID: 84990211388     PISSN: 87556863     EISSN: 10990496     Source Type: Journal    
DOI: 10.1002/ppul.23616     Document Type: Article

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