Survival of patients with spinal muscular atrophy type 1

Pediatrics

Volumn 131, Issue 5, 2013, Pages

  Gregoretti, Cesare ^a   Ottonello, Giancarlo ^b   Testa, Maria Beatrice Chiarini ^b   Mastella, Chiara ^c   Ravà, Lucilla ^b   Bignamini, Elisabetta ^d   Veljkovic, Aleksandar ^d   Cutrera, Renato ^b  

^a Città Della Salute e Della Scienza ^*  (Italy)

^b BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

^c FONDAZIONE IRCCS CA GRANDA OSPEDALE MAGGIORE POLICLINICO   (Italy)

^d Unit of Pneumology   (Italy)

Author keywords

Home mechanical ventilation; Long survival; Mechanical assisted cough; Pediatric palliative care; Spinal muscular atrophy type 1

Indexed keywords

AGE DISTRIBUTION; ARTICLE; ARTIFICIAL VENTILATION; CHILD; FEMALE; HUMAN; MAJOR CLINICAL STUDY; MALE; NONINVASIVE RESPIRATORY MUSCLE AID; NONINVASIVE VENTILATION; PRESCHOOL CHILD; PRIORITY JOURNAL; PROGNOSIS; RESPIRATORY FAILURE; RETROSPECTIVE STUDY; SPINAL MUSCULAR ATROPHY; SPINAL MUSCULAR ATROPHY TYPE 1; SURVIVAL; SURVIVAL RATE; TRACHEOSTOMY; TREATMENT OUTCOME;

HOME MECHANICAL VENTILATION; LONG SURVIVAL; MECHANICAL ASSISTED COUGH; PEDIATRIC PALLIATIVE CARE; SPINAL MUSCULAR ATROPHY TYPE 1;

CAUSE OF DEATH; CHILD, PRESCHOOL; COHORT STUDIES; CONFIDENCE INTERVALS; DATABASES, FACTUAL; FEMALE; HUMANS; INFANT; INFANT, NEWBORN; KAPLAN-MEIER ESTIMATE; MALE; NONINVASIVE VENTILATION; OXYGEN INHALATION THERAPY; PALLIATIVE CARE; PROGNOSIS; RESPIRATION, ARTIFICIAL; RETROSPECTIVE STUDIES; RISK ASSESSMENT; SEVERITY OF ILLNESS INDEX; SPINAL MUSCULAR ATROPHIES OF CHILDHOOD; STATISTICS, NONPARAMETRIC; SURVIVAL ANALYSIS;

EID: 84877066089     PISSN: 00314005     EISSN: 10984275     Source Type: Journal    
DOI: 10.1542/peds.2012-2278     Document Type: Article

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