Dystrophin Hot-Spot Mutants Leading to Becker Muscular Dystrophy Insert More Deeply into Membrane Models than the Native Protein

Biochemistry

Volumn 55, Issue 29, 2016, Pages 4018-4026

  Ameziane Le Hir, Sarah ^a,b,c   Paboeuf, Gilles ^a,b   Tascon, Christophe ^a,c   Hubert, Jean François ^a,c   Le Rumeur, Elisabeth ^a,c   Vié, Véronique ^a,b   Raguénès Nicol, Céline ^a,c  

^a UNIVERSITÉ DE RENNES 1   (France)

^b UNIVERSITÉ DE RENNES 1   (France)

^c UNIVERSITÉ DE RENNES 1   (France)

Author keywords

[No Author keywords available]

Indexed keywords

ATOMIC FORCE MICROSCOPY; DISSOCIATION; LIPOSOMES; MONOLAYERS; PATHOLOGY;

COILED-COIL STRUCTURE; DISSOCIATION CONSTANT; DUCHENNE MUSCULAR DYSTROPHIES; FULL-LENGTH PROTEINS; MOLECULAR BEHAVIOR; PROTEIN ADSORPTION; UNILAMELLAR LIPOSOMES; WILD-TYPE PROTEINS;

PROTEINS;

AMPHOPHILE; DYSTROPHIN; LIPOSOME; MUTANT PROTEIN; DMD PROTEIN, HUMAN; MEMBRANE LIPID; SPECTRIN;

ADSORPTION; ARTICLE; ATOMIC FORCE MICROSCOPY; BECKER MUSCULAR DYSTROPHY; CONTROLLED STUDY; DELETION MUTANT; DISSOCIATION CONSTANT; EXON; HYDROPHOBICITY; LIPID MONOLAYER; MEMBRANE MODEL; MICROSCALE THERMOPHORESIS; PRESSURE; PRIORITY JOURNAL; PROTEIN LIPID INTERACTION; PROTEIN STRUCTURE; SURFACE PROPERTY; THERMAL ANALYSIS; WILD TYPE; AMINO ACID REPEAT; CELL MEMBRANE; CHEMISTRY; DUCHENNE MUSCULAR DYSTROPHY; GENE DELETION; GENETICS; HUMAN; METABOLISM; MOLECULAR MODEL; MUTATION;

CELL MEMBRANE; DYSTROPHIN; EXONS; HUMANS; MEMBRANE LIPIDS; MICROSCOPY, ATOMIC FORCE; MODELS, MOLECULAR; MUSCULAR DYSTROPHY, DUCHENNE; MUTANT PROTEINS; MUTATION; REPETITIVE SEQUENCES, AMINO ACID; SEQUENCE DELETION; SPECTRIN; UNILAMELLAR LIPOSOMES;

EID: 84979964972     PISSN: 00062960     EISSN: 15204995     Source Type: Journal    
DOI: 10.1021/acs.biochem.6b00290     Document Type: Article

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