Disturbance of proteasomal and autophagic protein degradation pathways by amyotrophic lateral sclerosis-linked mutations in ubiquilin 2

Biochemical and Biophysical Research Communications

Volumn 472, Issue 2, 2016, Pages 324-331

  Osaka, Mayuko ^a   Ito, Daisuke ^a   Suzuki, Norihiro ^a  

^a KEIO UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

Amyotrophic lateral sclerosis; Autophagy; Frontotemporal dementia; Ubiquilin; Ubiquitin proteasome system

Indexed keywords

PROTEASOME; TAR DNA BINDING PROTEIN;

AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; AUTOPHAGY; CELLULAR DISTRIBUTION; GENE; GENE MUTATION; GENE OVEREXPRESSION; GENETIC ASSOCIATION; HUMAN; IMMUNOCYTOCHEMISTRY; NERVE CELL; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN DEGRADATION; UBIQUILIN GENE; UBIQUITINATION; ANIMAL; CELL LINE; GENETICS; METABOLISM; MOUSE; MUTATION; PATHOLOGY; SIGNAL TRANSDUCTION;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; AUTOPHAGY; CELL LINE; MICE; MUTATION; NEURONS; PROTEASOME ENDOPEPTIDASE COMPLEX; PROTEOLYSIS; SIGNAL TRANSDUCTION;

EID: 84959488435     PISSN: 0006291X     EISSN: 10902104     Source Type: Journal    
DOI: 10.1016/j.bbrc.2016.02.107     Document Type: Article

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