Total biliary diversion as a treatment option for patients with progressive familial intrahepatic cholestasis and Alagille syndrome

Journal of Pediatric Surgery

Volumn 50, Issue 11, 2015, Pages 1846-1849

  Van Der Woerd, Wendy L ^a   Kokke, Freddy T ^a   Van Der Zee, David C ^a   Houwen, Roderick H ^a  

^a UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

Author keywords

Alagille syndrome; Biliary diversion; Fat soluble vitamins; Malabsorption; Progressive familial intrahepatic cholestasis

Indexed keywords

ALANINE AMINOTRANSFERASE; ANTIBIOTIC AGENT; ASPARTATE AMINOTRANSFERASE; BILE ACID; BILIRUBIN; COTRIMOXAZOLE; GAMMA GLUTAMYLTRANSFERASE; VITAMIN K GROUP;

ABDOMINAL BLEEDING; ADULT; ALAGILLE SYNDROME; ANASTOMOSIS LEAKAGE; ANTIBIOTIC PROPHYLAXIS; ARTICLE; BILE DUCT BYPASS; BILIARY TRACT SURGERY; BIOCHEMICAL ANALYSIS; CHILD; CHOLANGITIS; CHOLECYSTOAPPENDICOSTOMY; CHOLECYSTOJEJUNOSTOMY; CHOLEDOCHAL DUCT LIGATION; CHOLEDOCHOJEJUNOSTOMY; CHOLESTASIS; CLINICAL ARTICLE; CLINICAL EFFECTIVENESS; COMMON BILE DUCT; DIARRHEA; END TO SIDE ANASTOMOSIS; FEMALE; FEVER; FOLLOW UP; HEPATOJEJUNOSTOMY; HUMAN; HUMAN TISSUE; INTRAHEPATIC CHOLESTASIS; MALABSORPTION; MALE; MIDDLE AGED; OUTCOME ASSESSMENT; PATIENT SAFETY; PRESCHOOL CHILD; PRIORITY JOURNAL; PRURITUS; SCHOOL CHILD; STENOSIS; STOMA; TISSUE INJURY; VITAMIN K DEFICIENCY; VITAMIN SUPPLEMENTATION; WEIGHT REDUCTION; YOUNG ADULT; ADOLESCENT; ANASTOMOSIS; CHOLESTASIS, INTRAHEPATIC; COMPLICATION; DEFICIENCY; ENZYMOLOGY; INFANT; JEJUNUM; LIVER; PROCEDURES;

ADOLESCENT; ALAGILLE SYNDROME; ANASTOMOSIS, SURGICAL; CHILD; CHILD, PRESCHOOL; CHOLESTASIS; CHOLESTASIS, INTRAHEPATIC; FEMALE; GAMMA-GLUTAMYLTRANSFERASE; HUMANS; INFANT; JEJUNUM; LIVER; MALE; PRURITUS; SURGICAL STOMAS;

EID: 84953362340     PISSN: 00223468     EISSN: 15315037     Source Type: Journal    
DOI: 10.1016/j.jpedsurg.2015.07.016     Document Type: Article

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