Normalization of serum bile acids after partial external biliary diversion indicates an excellent long-term outcome in children with progressive familial intrahepatic cholestasis

Journal of Pediatric Surgery

Volumn 47, Issue 3, 2012, Pages 501-505

  Schukfeh, Nagoud ^a   Metzelder, Martin Lothar ^a   Petersen, Claus ^a   Reismann, Marc ^a   Pfister, Eva Doreen ^a   Ure, Benno Manfred ^a   Kuebler, Joachim Friedrich ^a  

^a HANNOVER MEDICAL SCHOOL   (Germany)

Author keywords

glutamyltransferase; alanine aminotransferase; ALT; aspartate amino transferase; AST; bile salt export protein; BSEP; CHE; choline esterase; elastic van Giesson; EVG; familial intrahepatic cholestasis; FIC; GGT; GLDH; glutamate dehydrogenase; liver transplantation; LTX; PFIC; progressive familial intrahepatic cholestasis

Indexed keywords

ALANINE AMINOTRANSFERASE; ASPARTATE AMINOTRANSFERASE; BILE ACID; BILIRUBIN; CHOLINESTERASE; COTRIMOXAZOLE; GAMMA GLUTAMYLTRANSFERASE; GLUTAMATE DEHYDROGENASE; URSODEOXYCHOLIC ACID;

ARTICLE; BILE ACID BLOOD LEVEL; BILIARY TRACT SURGERY; CHILD; CLINICAL ARTICLE; DISEASE COURSE; FAMILIAL DISEASE; FOLLOW UP; HUMAN; INTRAHEPATIC CHOLESTASIS; LABORATORY TEST; LIVER CIRRHOSIS; LIVER TRANSPLANTATION; OUTCOME ASSESSMENT; PARTIAL EXTERNAL BILIARY DIVERSION; POSTOPERATIVE COMPLICATION; POSTOPERATIVE PERIOD; PRIORITY JOURNAL; PROGRESSIVE FAMILIAL INTRAHEPATIC CHOLESTASIS; PRURITUS; RETROSPECTIVE STUDY; RISK FACTOR; SURGICAL TECHNIQUE; SURVIVAL; TREATMENT FAILURE;

ADOLESCENT; BILE ACIDS AND SALTS; BILIARY TRACT SURGICAL PROCEDURES; BIOLOGICAL MARKERS; CHILD; CHILD, PRESCHOOL; CHOLESTASIS, INTRAHEPATIC; FEMALE; FOLLOW-UP STUDIES; HUMANS; INFANT; LIVER CIRRHOSIS; LIVER TRANSPLANTATION; MALE; OSTOMY; RETROSPECTIVE STUDIES; RISK FACTORS; TREATMENT OUTCOME;

EID: 84858202640     PISSN: 00223468     EISSN: 15315037     Source Type: Journal    
DOI: 10.1016/j.jpedsurg.2011.08.010     Document Type: Article

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