Alpha-1-antitrypsin deficiency panniculitis presenting with severe anasarca, pulmonary embolus and hypogammaglobulinaemia

British Journal of Dermatology

Volumn 173, Issue 1, 2015, Pages 289-291

  Elsensohn, A N ^a   Curtis, J A ^a   Secrest, A M ^a   Liaqat, M ^b   Florell, S R ^a   Duffy, K L ^a   Edholm, K ^a   Summers, E M ^a  

^a UNIVERSITY OF UTAH SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ALANINE AMINOTRANSFERASE; ALPHA 1 ANTITRYPSIN; ALPHA 1 ANTITRYPSIN CONCENTRATE; ASPARTATE AMINOTRANSFERASE; DAPSONE; PREDNISONE; ANTIINFLAMMATORY AGENT;

ACUTE FEBRILE NEUTROPHILIC DERMATOSIS; ADULT; ALANINE AMINOTRANSFERASE BLOOD LEVEL; ALPHA 1 ANTITRYPSIN DEFICIENCY; ALPHA 1 ANTITRYPSIN DEFICIENCY PANNICULITIS; ANASARCA; ASPARTATE AMINOTRANSFERASE BLOOD LEVEL; CASE REPORT; DOSE RESPONSE; DRUG MEGADOSE; DRUG TREATMENT FAILURE; ERYTHEMA NODOSUM; FEMALE; HUMAN; HUMAN TISSUE; HYPERTRANSAMINASEMIA; IMMUNOGLOBULIN DEFICIENCY; LETTER; LUNG EMBOLISM; PANNICULITIS; PRIORITY JOURNAL; SKIN BIOPSY; SKIN DEFECT; SKIN EDEMA; TREATMENT RESPONSE; AGAMMAGLOBULINEMIA; ALPHA 1-ANTITRYPSIN DEFICIENCY; COMPLICATION; DRUG ADMINISTRATION; DRUG COMBINATION; EDEMA; PULMONARY EMBOLISM; TREATMENT OUTCOME;

ADULT; AGAMMAGLOBULINEMIA; ALPHA 1-ANTITRYPSIN; ALPHA 1-ANTITRYPSIN DEFICIENCY; ANTI-INFLAMMATORY AGENTS; DAPSONE; DRUG ADMINISTRATION SCHEDULE; DRUG THERAPY, COMBINATION; EDEMA; FEMALE; HUMANS; PANNICULITIS; PULMONARY EMBOLISM; TREATMENT OUTCOME;

EID: 84948716818     PISSN: 00070963     EISSN: 13652133     Source Type: Journal    
DOI: 10.1111/bjd.13611     Document Type: Letter

References (11)

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