Report of the Tunisian Registry of Primary Immunodeficiencies: 25-Years of Experience (1988–2012)

Journal of Clinical Immunology

Volumn 35, Issue 8, 2015, Pages 745-753

  Mellouli, Fethi ^a,b   Mustapha, Imen Ben ^b,c   Khaled, Monia Ben ^a,b   Besbes, Habib ^a,b   Ouederni, Monia ^a,b   Mekki, Najla ^b,c   Ali, Meriem Ben ^b,c   Larguèche, Beya ^b,c   Hachicha, Mongia ^d   Sfar, Tahar ^e   Gueddiche, Neji ^f   Barsaoui, Siheme ^g   Sammoud, Azza ^g   Boussetta, Khadija ^g   Becher, Saida Ben ^g   Meherzi, Ahmed ^h   Guandoura, Najoua ⁱ   Boughammoura, Lamia ^j   Harbi, Abdelaziz ^k   Amri, Fethi ^l   Bayoudh, Fethi ^m   Jaballah, Najla Ben ^g   Tebib, Neji ⁿ   Bouaziz, Asma ^o   Mahfoudh, Abdelmajid ^d   Aloulou, Hajer ^d   Mansour, Lamia Ben ^d   Chabchoub, Imen ^d   Boussoffara, Raoudha ^e   Chemli, Jalel ^k   Bouguila, Jihène ^j   Hassayoun, Saida ^k   Hammami, Saber ^f   Habboul, Zakia ^f   Hamzaoui, Agnès ^p   Ammar, Jamel ^p   Barbouche, Mohamed Ridha ^b,c   Bejaoui, Mohamed ^a,b   more..

^a CENTRE NATIONAL DE GREFFE DE MOELLE OSSEUSE   (Tunisia)

^b UNIVERSITY OF TUNIS EL MANAR   (Tunisia)

^c PASTEUR INSTITUTE OF TUNIS   (Tunisia)

^d UNIVERSITY OF SFAX   (Tunisia)

^e hôpital de Mehdia   (Tunisia)

^f FATTOUMA BOURGUIBA UNIVERSITY HOSPITAL   (Tunisia)

^g CHILDREN S HOSPITAL   (Tunisia)

^h MONGI SLIM HOSPITAL   (Tunisia)

ⁱ Regional Hospital of Bizerte   (Tunisia)

^j FARHAT HACHED HOSPITAL   (Tunisia)

^k SAHLOUL UNIVERSITY HOSPITAL   (Tunisia)

^l Hopital Regional de Kairouan   (Tunisia)

^m MILITARY HOSPITAL OF TUNIS   (Tunisia)

ⁿ LA RABTA HOSPITAL   (Tunisia)

^o Hopital Mohamed Tahar Maamouri   (Tunisia)

^p Hôpital de l'Ariana   (Tunisia)

more..

Author keywords

diagnosis; management; Primary immunodeficiencies; treatments; Tunisia

Indexed keywords

IMMUNOGLOBULIN; ANTIBODY; COMPLEMENT;

AGAMMAGLOBULINEMIA; ALLOGENEIC HEMATOPOIETIC STEM CELL TRANSPLANTATION; ARTICLE; ATAXIA TELANGIECTASIA; AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME; BARE LYMPHOCYTE SYNDROME; BUCKLEY SYNDOME; CELLULAR IMMUNODEFICIENCY; CHEDIAK HIGASHI SYNDROME; CHILD; CHRONIC GRANULOMATOUS DISEASE; CLINICAL FEATURE; COMBINED IMMUNODEFICIENCY; COMMON VARIABLE IMMUNODEFICIENCY; COMPLEMENT DEFICIENCY; CONSANGUINITY; DIGEORGE SYNDROME; DISEASE CLASSIFICATION; DISEASE REGISTRY; FAMILIAL LYMPHOHISTIOCYTIC HEMOPHAGOCYTOSIS; FEMALE; GRISCELLI SYNDROME; HUMAN; HUMORAL IMMUNE DEFICIENCY; HYPER IGM SYNDROME; IMMUNE DEFICIENCY; IMMUNE DYSREGULATION; IMMUNOGLOBULIN A DEFICIENCY; IMMUNOGLOBULIN G DEFICIENCY; INFANT; LEUKOCYTE ADHESION DEFICIENCY; LOWER RESPIRATORY TRACT INFECTION; MAJOR CLINICAL STUDY; MALE; MEDICAL RECORD REVIEW; MENDELIAN SUSCEPTIBILITY TO MYCOBACTERIAL DISEASE; MORTALITY; NETHERTON DISEASE; NEUTROPENIA; OCULAR ALBINISM; OMENN SYNDROME; ONSET AGE; OUTCOME ASSESSMENT; PHAGOCYTE DYSFUNCTION; PREVALENCE; PRIORITY JOURNAL; PROGNOSIS; PURINE NUCLEOSIDE PHOSPHORYLASE DEFICIENCY; QUALITY OF LIFE; RECURRENT INFECTION; SEX RATIO; TERTIARY CARE CENTER; TUNISIA; TUNISIAN; UPPER RESPIRATORY TRACT INFECTION; WART HYPOGAMMAGLOBULINEMIA INFECTIONS MYELOKATHEXIS SYNDROME; WISKOTT ALDRICH SYNDROME; X LINKED LYMPHOPROLIFERATIVE SYNDROME; B LYMPHOCYTE; CLASSIFICATION; GENETICS; IMMUNOLOGIC DEFICIENCY SYNDROMES; METABOLISM; PHYSIOLOGY; REGISTER; SURVIVAL ANALYSIS; T LYMPHOCYTE;

AGE OF ONSET; ANTIBODIES; B-LYMPHOCYTES; COMPLEMENT SYSTEM PROTEINS; CONSANGUINITY; FEMALE; HUMANS; IMMUNOLOGIC DEFICIENCY SYNDROMES; INFANT; MALE; PREVALENCE; REGISTRIES; SURVIVAL ANALYSIS; T-LYMPHOCYTES; TUNISIA;

EID: 84948570918     PISSN: 02719142     EISSN: 15732592     Source Type: Journal    
DOI: 10.1007/s10875-015-0206-9     Document Type: Article

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