Hepatic glycogen storage disorders: What have we learned in recent years?

Current Opinion in Clinical Nutrition and Metabolic Care

Volumn 18, Issue 4, 2015, Pages 415-421

  Burda, Patricie ^a,b   Hochuli, Michel ^b,c  

^a UNIVERSITY CHILDREN S HOSPITAL   (Switzerland)

^b UNIVERSITY HOSPITAL ZURICH   (Switzerland)

^c UNIVERSITY OF ZURICH   (Switzerland)

Author keywords

Complications; Glycogen storage disease; Hypoglycemia; Liver; Metabolic control; Outcome

Indexed keywords

ANEMIA; BONE DENSITY; CHRONIC KIDNEY DISEASE; GLUCONEOGENESIS; GLYCOGEN LIVER LEVEL; GLYCOGEN STORAGE DISEASE; GLYCOGEN STORAGE DISEASE TYPE 1; GLYCOGEN STORAGE DISEASE TYPE 3; GLYCOGEN STORAGE DISEASE TYPE 4; GLYCOGEN STORAGE DISEASE TYPE 9; HUMAN; LIVER ADENOMA; METABOLIC REGULATION; NEXT GENERATION SEQUENCING; REVIEW; ADMINISTRATION AND DOSAGE; ANIMAL; CARBOHYDRATE DIET; CARDIOMYOPATHY; COMPLICATION; DIET THERAPY; DISEASE MODEL; FAT INTAKE; GLYCOGEN STORAGE DISEASE TYPE I; GLYCOGEN STORAGE DISEASE TYPE III; GLYCOGEN STORAGE DISEASE TYPE VI; LIPID DIET; LIVER; LIVER CIRRHOSIS; LOW CARBOHYDRATE DIET; METABOLISM; PATHOPHYSIOLOGY; PROTEIN INTAKE;

CARBOHYDRATE DIET; FAT INTAKE; GLYCOGEN; PROTEIN INTAKE;

ANIMALS; CARDIOMYOPATHIES; DIET, CARBOHYDRATE-RESTRICTED; DIET, HIGH-FAT; DIETARY CARBOHYDRATES; DIETARY FATS; DIETARY PROTEINS; DISEASE MODELS, ANIMAL; GLYCOGEN; GLYCOGEN STORAGE DISEASE TYPE I; GLYCOGEN STORAGE DISEASE TYPE III; GLYCOGEN STORAGE DISEASE TYPE VI; HUMANS; LIVER; LIVER CIRRHOSIS;

EID: 84942782010     PISSN: 13631950     EISSN: 14736519     Source Type: Journal    
DOI: 10.1097/MCO.0000000000000181     Document Type: Review

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