Impaired bone metabolism in glycogen storage disease type 1 is associated with poor metabolic control in type 1a and with granulocyte colony-stimulating factor therapy in type 1b

Hormone Research in Paediatrics

Volumn 81, Issue 1, 2014, Pages 55-62

  Melis, D ^a   Pivonello, R ^a   Cozzolino, M ^a   Della Casa, R ^a   Balivo, F ^a   Del Puente, A ^a   Dionisi Vici, C ^b   Cotugno, G ^b   Zuppaldi, C ^a   Rigoldi, M ^c   Parini, R ^c   Colao, A ^a   Andria, G ^a   Parenti, G ^a  

^a UNIVERSITY OF NAPLES FEDERICO II   (Italy)

^b BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

^c SAN GERARDO HOSPITAL   (Italy)

Author keywords

Bone metabolism; Bone mineral density; Glycogen storage disease type 1a; Glycogen storage disease type 1b; Granulocyte colony stimulating factor; Metabolic control

Indexed keywords

ALLOPURINOL; GRANULOCYTE COLONY STIMULATING FACTOR; MESALAZINE;

ABSORPTIOMETRY; ADOLESCENT; ARTICLE; BONE DENSITY; BONE METABOLISM; CASE CONTROL STUDY; CLINICAL ARTICLE; CONTROLLED STUDY; DIET; FEMALE; GENE; GLYCOGEN STORAGE DISEASE TYPE 1; HUMAN; HYPERURICEMIA; INFLAMMATION; IRRITABLE COLON; MALE; METABOLIC REGULATION; OSTEOPENIA; OSTEOPOROSIS; PRIORITY JOURNAL; SLC37A4 GENE; X RAY; CHILD; DUAL ENERGY X RAY ABSORPTIOMETRY; ECHOGRAPHY; MULTICENTER STUDY; PATIENT COMPLIANCE; SCHOOL CHILD; TREATMENT DURATION; BONE; BONE DISEASES, METABOLIC; CHEMICALLY INDUCED; CLINICAL TRIAL; CROSS-SECTIONAL STUDY; DIET THERAPY; GLYCOGEN STORAGE DISEASE TYPE I; GROWTH DISORDERS; METABOLISM; STATISTICS AND NUMERICAL DATA;

ADOLESCENT; BONE AND BONES; BONE DENSITY; BONE DISEASES, METABOLIC; CASE-CONTROL STUDIES; CHILD; CROSS-SECTIONAL STUDIES; FEMALE; GLYCOGEN STORAGE DISEASE TYPE I; GRANULOCYTE COLONY-STIMULATING FACTOR; GROWTH DISORDERS; HUMANS; MALE; PATIENT COMPLIANCE;

EID: 84897023533     PISSN: 16632818     EISSN: 16632826     Source Type: Journal    
DOI: 10.1159/000351022     Document Type: Article

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