Tuberous Sclerosis Complex: State-of-the-Art Review with a Focus on Pulmonary Involvement

Lung

Volumn 193, Issue 5, 2015, Pages 619-627

  von Ranke, Felipe Mussi ^a   Zanetti, Gláucia ^a   e Silva, Jorge Luiz Pereira ^b   Neto, Cesar Augusto Araujo ^b   Godoy, Myrna C B ^c   Souza, Carolina A ^d   Mançano, Alexandre Dias ^e   Souza, Arthur Soares ^f   Escuissato, Dante Luiz ^g   Hochhegger, Bruno ^h   Marchiori, Edson ^a  

^a FEDERAL UNIVERSITY OF RIO DE JANEIRO   (Brazil)

^b FEDERAL UNIVERSITY OF BAHIA   (Brazil)

^c UNIVERSITY OF TEXAS MD ANDERSON CANCER CENTER   (United States)

^d OTTAWA HOSPITAL RESEARCH INSTITUTE   (Canada)

^e Anchieta Hospital   (Brazil)

^f Rio Preto Medical School   (Brazil)

^g FEDERAL UNIVERSITY OF PARANÁ   (Brazil)

^h Santa Casa de Porto Alegre   (Brazil)

Author keywords

Computed tomography; Imaging; Lung diseases; Lymphangioleiomyomatosis; Tuberous sclerosis complex

Indexed keywords

BIRT HOGG DUBE SYNDROME; CELL DIFFERENTIATION; CELL PROLIFERATION; DISEASE COURSE; GENETIC SCREENING; GERMLINE MUTATION; HUMAN; INCIDENCE; INTELLECTUAL IMPAIRMENT; INTERSTITIAL PNEUMONIA; KIDNEY CARCINOMA; KIDNEY CYST; KIDNEY HEMANGIOMYOLIPOMA; LANGERHANS CELL HISTIOCYTOSIS; LUNG BIOPSY; LUNG DISEASE; LYMPHANGIOLEIOMYOMATOSIS; NEUROLOGICAL COMPLICATION; PHAKOMATOSIS; PRIORITY JOURNAL; REGULATORY MECHANISM; REVIEW; RHABDOMYOMA; SEIZURE; SKIN DEFECT; SUBEPENDYMAL GIANT CELL ASTROCYTOMA; TUBEROUS SCLEROSIS; ANGIOMYOLIPOMA; CARCINOMA, RENAL CELL; COMPLICATION; CYSTS; HYPERPLASIA; KIDNEY NEOPLASMS; LUNG; LUNG NEOPLASMS; NERVOUS SYSTEM DISEASES; PATHOLOGY; SKIN DISEASES;

ANGIOMYOLIPOMA; CARCINOMA, RENAL CELL; CYSTS; HUMANS; HYPERPLASIA; KIDNEY NEOPLASMS; LUNG; LUNG NEOPLASMS; LYMPHANGIOLEIOMYOMATOSIS; NERVOUS SYSTEM DISEASES; SKIN DISEASES; TUBEROUS SCLEROSIS;

EID: 84942502746     PISSN: 03412040     EISSN: 14321750     Source Type: Journal    
DOI: 10.1007/s00408-015-9750-6     Document Type: Review

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