Leaky RAG deficiency in adult patients with impaired antibody production against bacterial polysaccharide antigens

PLoS ONE

Volumn 10, Issue 7, 2015, Pages

  Geier, Christoph B ^a   Piller, Alexander ^a   Linder, Angela ^a   Sauerwein, Kai M T ^a   Eibl, Martha M ^a,b   Wolf, Hermann M ^a  

^a Immunology Outpatient Clinic ^*  (Austria)

^b Biomedizinische Forschungsgesellschaft mbH   (Austria)

Author keywords

[No Author keywords available]

Indexed keywords

BACTERIAL ANTIGEN; BACTERIAL POLYSACCHARIDE; IMMUNOGLOBULIN A; IMMUNOGLOBULIN G ANTIBODY; IMMUNOGLOBULIN G2; IMMUNOGLOBULIN G3; IMMUNOGLOBULIN G4; IMMUNOGLOBULIN M ANTIBODY; RAG1 PROTEIN; RAG2 PROTEIN; DNA BINDING PROTEIN; HOMEODOMAIN PROTEIN; LIPOPOLYSACCHARIDE; NUCLEAR PROTEIN; RAG-1 PROTEIN; RAG2 PROTEIN, HUMAN;

ADULT; ALLELE; ANTIBODY PRODUCTION; ANTIBODY RESPONSE; ARTICLE; BACTERIAL INFECTION; BRONCHITIS; CARBOXY TERMINAL SEQUENCE; CASE REPORT; CD4 LYMPHOCYTE COUNT; CELL DIFFERENTIATION; CLINICAL FEATURE; CODON; CONTROLLED STUDY; FEMALE; GENE AMPLIFICATION; GENE EXPRESSION; GENE MUTATION; HUMAN; HUMAN CELL; HUMAN TISSUE; HUMORAL IMMUNE DEFICIENCY; IMMUNE DEFICIENCY; IMMUNOGLOBULIN BLOOD LEVEL; IMMUNOGLOBULIN DEFICIENCY; INFECTION SENSITIVITY; INTERSTITIAL PNEUMONIA; LEUKOCYTOCLASTIC VASCULITIS; LOWER RESPIRATORY TRACT INFECTION; LUNG BIOPSY; MOLECULAR CLONING; OTITIS MEDIA; PROTEIN EXPRESSION; RAG1 GENE; RAG2 GENE; RECURRENT DISEASE; SINUSITIS; STREPTOCOCCUS PNEUMONIAE; SUBSTITUTION THERAPY; TREATMENT RESPONSE; UPPER RESPIRATORY TRACT INFECTION; CD4+ T LYMPHOCYTE; GENETICS; IMMUNOLOGIC DEFICIENCY SYNDROMES; IMMUNOLOGY; METABOLISM; MUTATION;

ADULT; CD4-POSITIVE T-LYMPHOCYTES; DNA-BINDING PROTEINS; FEMALE; HOMEODOMAIN PROTEINS; HUMANS; IMMUNOLOGIC DEFICIENCY SYNDROMES; LIPOPOLYSACCHARIDES; MUTATION; NUCLEAR PROTEINS;

EID: 84941308408     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0133220     Document Type: Article

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