Association of sweat chloride concentration at time of diagnosis and CFTR genotype with mortality and cystic fibrosis phenotype

Journal of Cystic Fibrosis

Volumn 14, Issue 5, 2015, Pages 580-586

  McKone, Edward F ^a   Velentgas, Priscilla ^b   Swenson, Anna J ^b   Goss, Christopher H ^c  

^a ST VINCENT S UNIVERSITY HOSPITAL   (Ireland)

^b IQVIA   (United States)

^c UNIVERSITY OF WASHINGTON   (United States)

Author keywords

Cystic fibrosis; Genetics; Respiratory function; Survival analysis

Indexed keywords

CHLORIDE; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR;

ADOLESCENT; ADULT; ARTICLE; BODY HEIGHT; BODY MASS; BODY WEIGHT; CHILD; CYSTIC FIBROSIS; DISEASE COURSE; FEMALE; FOLLOW UP; FORCED EXPIRATORY VOLUME; GENOTYPE; GROWTH; HUMAN; LUNG DISEASE; LUNG FUNCTION; MAJOR CLINICAL STUDY; MALE; MORTALITY; NUTRITIONAL STATUS; PHENOTYPE; SURVIVAL; SWEAT; CHEMISTRY; CLINICAL TRIAL; EPIDEMIOLOGY; GENETICS; METABOLISM; MULTICENTER STUDY; MUTATION; PRESCHOOL CHILD; PROGNOSIS; PROPORTIONAL HAZARDS MODEL; RETROSPECTIVE STUDY; SURVIVAL RATE; TRENDS; UNITED STATES;

ADOLESCENT; CHILD; CHILD, PRESCHOOL; CHLORIDES; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; FEMALE; FOLLOW-UP STUDIES; GENOTYPE; HUMANS; MALE; MUTATION; PHENOTYPE; PROGNOSIS; PROPORTIONAL HAZARDS MODELS; RETROSPECTIVE STUDIES; SURVIVAL RATE; SWEAT; UNITED STATES;

EID: 84940955117     PISSN: 15691993     EISSN: 18735010     Source Type: Journal    
DOI: 10.1016/j.jcf.2015.01.005     Document Type: Article

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