A case of variably protease-sensitive prionopathy treated with doxycyclin

Journal of Neurology, Neurosurgery and Psychiatry

Volumn 86, Issue 7, 2015, Pages 816-818

  Assar, Hamid ^a   Topakian, Raffi ^b   Weis, Serge ^a   Rahimi, Jasmin ^c   Trenkler, Johannes ^a   Höftberger, Romana ^c   Aboulenein Djamshidian, Fahmy ^d   Ströbel, Thomas ^c   Budka, Herbert ^e   Yull, Helen ^f   Head, Mark W ^f   Ironside, James W ^f   Kovacs, Gabor G ^c  

^a JOHANNES KEPLER UNIVERSITY LINZ   (Austria)

^b Klinikum Wels Grieskirchen GmbH   (Austria)

^c MEDICAL UNIVERSITY OF VIENNA   (Austria)

^d DANUBE HOSPITAL   (Austria)

^e UNIVERSITY HOSPITAL ZURICH   (Switzerland)

^f UNIVERSITY OF EDINBURGH   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

DOXYCYCLINE; ANTIINFECTIVE AGENT;

BRAIN SPONGIOSIS; DEGENERATIVE DISEASE; HUMAN; LETTER; PRIORITY JOURNAL; VARIABLY PROTEASE SENSITIVE PRIONOPATHY; BRAIN; CASE REPORT; DIFFUSION WEIGHTED IMAGING; FEMALE; MIDDLE AGED; PATHOLOGY; PRION DISEASES; TREATMENT OUTCOME;

ANTI-BACTERIAL AGENTS; BRAIN; DIFFUSION MAGNETIC RESONANCE IMAGING; DOXYCYCLINE; FEMALE; HUMANS; MIDDLE AGED; PRION DISEASES; TREATMENT OUTCOME;

EID: 84939239868     PISSN: 00223050     EISSN: 1468330X     Source Type: Journal    
DOI: 10.1136/jnnp-2014-309871     Document Type: Letter

References (5)

1. Zou WQ, Puoti G, Xiao X, et al. Variably protease-sensitive prionopathy: a new sporadic disease of the prion protein. Ann Neurol 2010; 68: 162-72.
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3. Kovacs GG, Peden A, Weis S, et al. Rapidly progressive dementia with thalamic degeneration and peculiar cortical prion protein immunoreactivity, but absence of proteinase K resistant PrP: a new disease entity? Acta Neuropathol Commun 2013; 1: 72.
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